Abnormal Branching Pattern Of The Aortic Arch C4023282
A congenital abnormality in aortic arch branching patterns. Can affect anyone with this variant. Treatment depends on symptoms.
Key facts at a glance
- ICD-10
- I78.0
- ICD-11
- BA00.0
- Body system
- cardiovascular
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Cyanosis
Bluish discoloration of the skin and lips indicating inadequate oxygen supply, occurring in severe cases with significant airway obstruction.
Cyanosis is a medical emergency. Seek immediate emergency care.
Noisy breathing (stridor)
(respiratory)High-pitched breathing sound caused by narrowing of the trachea due to compression from the abnormal aortic arch branch.
Frequency: 60-70% of patients
Difficulty swallowing (dysphagia)
(gastrointestinal)Sensation of food sticking in the throat or chest due to compression of the esophagus by the abnormal vascular structure.
Frequency: 50-60% of patients
Shortness of breath
(respiratory)Feeling of breathlessness or air hunger resulting from tracheal compression or airway obstruction caused by the abnormal vessel.
Frequency: 30-40% of patients
Chronic cough
(respiratory)Persistent cough that does not go away, often due to irritation or compression of the airway by the abnormal aortic arch branch.
Frequency: 40-50% of patients
Chest pain
(cardiovascular)Discomfort or pain in the chest area that may occur due to compression of cardiovascular structures by the abnormal branching pattern.
Frequency: 20-30% of patients
Hoarseness
(neurologic)Changes in voice quality including raspiness or weakness, often caused by compression of the recurrent laryngeal nerve.
Frequency: 15-25% of patients
Recurrent respiratory infections
(respiratory)Frequent lung or airway infections resulting from impaired airway clearance due to tracheal compression.
Frequency: 10-20% of patients
Wheezing
(respiratory)Whistling sound during breathing that may be mistaken for asthma but is caused by airway narrowing from vascular compression.
Frequency: 10-15% of patients
Difficulty feeding (infants)
(cardiovascular)In infants, difficulty with feeding or poor weight gain due to combined esophageal compression and respiratory compromise.
Frequency: 5% or fewer patients
Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Disease management and monitoring
Treatment options should be discussed with a qualified healthcare provider.
Vascular imaging surveillance
Regular CT angiography or MR angiography to monitor the aortic arch branching pattern and detect progressive changes.
Comprehensive cardiac evaluation
Detailed assessment including echocardiography and cardiac catheterization to determine functional significance and plan management.
When to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Abnormal Branching Pattern Of The Aortic Arch C4023282?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
American College of Radiology. ACR Appropriateness Criteria: Thoracic Aorta Interrogation. Reston, VA: ACR; 2022.
Jakanani G, Botnar R, Redpath T, et al. Imaging of the thoracic aorta: anatomy, pathology and MRI techniques. J Cardiovasc Med. 2012;13(8):481-490.
Popoff AM, Woo K, Malgieri N, et al. Aortic arch variants and anomalies. Ann Vasc Surg. 2020;69:120-134.
Liang W, Yu T, Liu J, et al. Multidetector CT angiography of aortic arch branching patterns: classification and clinical significance. J Vasc Surg. 2018;68(3):735-742.
Standring S, ed. Gray's Anatomy: The Anatomical Basis of Clinical Practice. 42nd ed. Elsevier; 2021.
Erbel R, Aboyans V, Boileau C, et al. 2014 ESC Guidelines on the diagnosis and treatment of aortic diseases. Eur Heart J. 2014;35(41):2873-2926.
Maldonado T, D'Ayala M, Radhakrishnan S, et al. Vascular rings and aortic arch anomalies: embryology and imaging. Cardiol Young. 2020;30(6):779-789.
Hiratzka LF, Bakris GL, Beckman JA, et al. 2010 ACCF/AHA/AATS/ACR/ASA/SCA/SCAI/SIR/STS/SVM Guidelines for the diagnosis and management of patients with thoracic aortic disease. Circulation. 2010;121(13):e266-e369.
Kau T, Sinzig M, Gasser J, et al. Aortic development and anomalies. Semin Intervent Radiol. 2007;24(2):141-152.
Duran C, Kantarci M, Durak M, et al. Multidetector CT angiography of aortic arch variants: a systematic review. Surg Radiol Anat. 2012;34(8):715-728.
Medication Comparisons
Compare medications used to treat Abnormal Branching Pattern Of The Aortic Arch C4023282. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy