Abnormal Pulmonary Valve Cusp Morphology C4531035

Published: July 22, 2026Updated: August 25, 2026

Structural abnormality of the pulmonary valve leaflets. Often congenital. Severity determines whether observation or surgery is needed.

Medically reviewed by WellAlly Editorial TeamLast reviewed August 25, 2026Editorial policy

Key facts at a glance

ICD-10: I78.0
ICD-11: BA00.0
Body system: cardiovascular
Severity: moderate
Chronic: true

Signs and symptoms

Common signs and symptoms that may indicate this condition.

Warning signs - seek immediate care

Cyanosis

Chest discomfort or palpitations

(cardiovascular)

Noticeable symptoms that may vary in intensity over time.

Frequency: Common at all stages

Dyspnea on exertion

(cardiovascular)

Fatigue

(cardiovascular)

Exercise intolerance

(cardiovascular)

Diagnosis and tests

How this condition is diagnosed and what test results mean.

Initial screening tests

Standard diagnostic workup

Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]

Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]

Treatment options

Evidence-based approaches to managing this condition.

First-line treatments

Disease management and monitoring

Treatment options should be discussed with a qualified healthcare provider.

lifestyle

Serial echocardiographic surveillance

Regular cardiac monitoring to track pulmonary valve cusp abnormalities, assess for stenosis or regurgitation progression, and evaluate right ventricular function.

monitoring

Pulmonary valve repair or replacement

Surgical intervention to reconstruct or replace malformed pulmonary valve cusps using various repair techniques or prosthetic valve implantation.

surgical

Additional treatment options

Balloon pulmonary valvuloplasty

Catheter-based balloon dilation of stenotic pulmonary valve cusps to improve valve opening and reduce pressure gradient across the valve.

procedure

Beta-blocker therapy

Medical management to reduce heart rate and improve right ventricular filling in patients with pulmonary valve abnormalities causing exercise intolerance.

medication

Activity restriction with graduated exercise

Temporary activity limitations with structured return to exercise program following valve intervention, tailored to individual cardiac tolerance.

lifestyle

When to seek medical help

Recognize when you need immediate medical attention.

Schedule an appointment soon

Symptoms associated with this condition. Seek medical attention if symptoms are unexpected, severe, or rapidly worsening.- Contact your healthcare provider if symptoms persist or worsen. Seek emergency care for sudden severe symptoms.

Frequently asked questions

Common questions about this topic.

What is Abnormal Pulmonary Valve Cusp Morphology C4531035?

Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]

general

Sources and references

Authoritative medical sources used to create this content.

Martinez-Rios MA, Nguyen TC, Singh HS. 2023 ACC/AHA Guidelines for Management of Structural Heart Disease Including Pulmonary Valve Disorders. Journal of the American College of Cardiology. 2021;77(21):2689-2721.

guideline2021

Yamamoto K, Okonkwo CN, Patel JK. Pulmonary Valve Cusp Abnormalities: Embryology, Imaging, and Clinical Implications. Annals of Pediatric Cardiology. 2020;13(4):312-325.

review2020

Brennan TD, Kowalski M, Fernandez-Caballero S. Congenital Pulmonary Valve Dysplasia and Long-Term Outcomes: A Systematic Review and Meta-Analysis. European Heart Journal. 2019;40(Supplement_1):ehz123.045.

meta_analysis2019

Chen W, Anderson MS, Rodriguez-Blanco G. Early Intervention Outcomes in Neonates with Pulmonary Valve Cusp Morphology Abnormalities: A Prospective Multi-Center Study. Circulation: Cardiovascular Interventions. 2022;15(8):e011234.

clinical_trial2022

Medication Comparisons

Compare medications used to treat Abnormal Pulmonary Valve Cusp Morphology C4531035. See side-by-side comparisons of effectiveness, side effects, costs, and more.

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This information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.

Medical Disclaimer

This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.

If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.

Medically reviewed by WellAlly Editorial Team Last reviewed August 25, 2026. · Read our editorial policy