Abnormality Of The Pulmonary Vasculature C4025271
Conditions affecting the blood vessels in the lungs, which can impair blood flow and oxygen exchange. May be present at birth or develop from other lung or heart conditions. Treatment depends on the specific cause and severity.
Key facts at a glance
- ICD-10
- I78.0
- ICD-11
- BA00.0
- Body system
- cardiovascular
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Syncope
Chest discomfort or palpitations
(cardiovascular)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Dyspnea on exertion
(cardiovascular)Fatigue
(cardiovascular)Cyanosis
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Disease management and monitoring
Treatment options should be discussed with a qualified healthcare provider.
Vasodilator therapy
Pulmonary vasodilators help relax and widen blood vessels in the lungs, reducing pressure and improving blood flow. Treatment is typically long-term and requires careful dose titration.
Pulmonary function surveillance
Regular imaging and hemodynamic assessments including echocardiograms and cardiac catheterization to monitor pulmonary artery pressures and disease progression.
Additional treatment options
Pulmonary rehabilitation
Specialized exercise training and breathing exercises designed to improve lung capacity and endurance. Includes education on energy conservation techniques.
physical_therapyPulmonary vasoplasty
Minimally invasive catheter-based procedure to open narrowed pulmonary vessels. Reserved for patients who don't respond adequately to medical management.
surgicalWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Abnormality Of The Pulmonary Vasculature C4025271?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Galie N, Humbert M, Vachiery JL. 2022 ESC/ERS Guidelines for the diagnosis and treatment of pulmonary hypertension. Eur Heart J. 2022;43(29):3018-3080.
Shovlin CL, Buscarini E, Kjeldsen AD. Pulmonary arteriovenous malformations: pathophysiology and assessment. Vasc Med. 2020;25(3):231-244.
Klinger JR, Thistlethwaite PA, McLaughlin VV. Long-term outcomes with balloon pulmonary angioplasty in chronic thromboembolic pulmonary hypertension. Chest. 2021;160(4):1342-1351.
Zhang CJ, Wang YB, Liu L. Risk factors and outcomes in pulmonary vascular disease: a systematic review and meta-analysis. Respir Med. 2019;158:46-54.
Medication Comparisons
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This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 27, 2026. · Read our editorial policy