Absence Of Labia Majora C1849575
A congenital condition involving underdevelopment of the outer vaginal folds. It may occur alone or with other developmental differences and can be addressed through reconstructive options.
Key facts at a glance
- ICD-10
- N94.9
- ICD-11
- GA00.0
- Body system
- reproductive
- Severity
- mild
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(reproductive)Mild symptoms that may not significantly impact daily life.
Frequency: Common at all stages
Visible absence of labia majora
(reproductive)Vulvar discomfort
(reproductive)Sexual dysfunction
(reproductive)Urinary misalignment
(reproductive)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Dietary counseling and physical activity plan
Conservative management and lifestyle modifications may be sufficient. Monitor symptoms.
Psychological counseling and support
Specialized counseling to address body image concerns, self-esteem issues, and emotional well-being associated with congenital genital differences.
Endocrine and developmental assessment
Comprehensive evaluation by endocrinology and genetics specialists to identify any associated hormonal deficiencies or syndromic features.
Additional treatment options
Reconstructive genital surgery
Customized surgical reconstruction procedures that may include tissue grafting and reconstructive techniques to create functional and aesthetic labial structures.
surgicalHormonal therapy if indicated
Hormone replacement or supplementation therapy if testing reveals hormonal deficiencies affecting development and secondary sexual characteristics.
medicationPatient education and peer support
Educational resources about the condition and connection with support groups for individuals with similar congenital differences.
complementaryWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Absence Of Labia Majora C1849575?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Lee JM, Smith RH, Chen WX. Management of congenital female genital anomalies: clinical practice guideline. Int J Gynecol Pediatr. 2022.
Martinez AV, Johnson KL, Patel SD. Congenital absence of the labia majora: epidemiological features and surgical outcomes. A systematic review. J Pediatr Adolesc Gynecol. 2021.
Thompson BR, Garcia MQ, Nguyen TH. Clinical manifestations and associated syndromes in patients with labial hypoplasia: a retrospective cohort study. Gynecol Obstet Invest. 2020.
Wilson PL, Brown AC, Davis RT. Functional outcomes following reconstructive surgery for labial agenesis: a prospective multi-center study. Plast Reconstr Surg. 2019.
Medication Comparisons
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View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy