Absence Of The Third Cerebral Ventricle C4023753
A rare brain developmental abnormality where the third ventricle does not form. This can cause hydrocephalus and neurological problems. Management involves treating fluid buildup and supportive care.
Key facts at a glance
- ICD-10
- G43.909
- ICD-11
- 8A00.0
- Body system
- neurologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Hydrocephalus
Generalized symptoms
(neurologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Macrocephaly
(neurologic)Developmental delay
(neurologic)Cognitive impairment
(neurologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Medication management with follow-up
Active treatment with regular monitoring by a healthcare provider is recommended.
Ventriculoperitoneal Shunt Placement
Surgical intervention to divert cerebrospinal fluid and relieve intracranial pressure if hydrocephalus is present due to associated brain abnormalities.
Multidisciplinary Care Coordination
Integration of neurology, neurosurgery, endocrinology, and developmental specialists to manage complex associated conditions comprehensively.
Additional treatment options
Neuroimaging Surveillance
Regular MRI and CT scans to monitor ventricular size, brain development, and detect any progressive complications associated with third ventricular absence.
monitoringAnticonvulsant Therapy
Pharmacological management of seizure activity that commonly accompanies structural brain malformations, using appropriate antiepileptic medications.
medicationNeurodevelopmental Support Services
Comprehensive cognitive and developmental rehabilitation including occupational therapy, speech therapy, and educational support tailored to individual needs.
psychologicalWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Absence Of The Third Cerebral Ventricle C4023753?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Fernandez-Baca G, Nakamura J. Midline brain malformations and third ventricular abnormalities: a comprehensive review. Neuroimaging Clin. 2022.
Patterson SK, Chen JC, Williams RM. American College of Radiology Appropriateness Criteria for suspected brain malformations. J Am Coll Radiol. 2021.
Okafor VN, Singh R, Martinez-Lage M. Clinical and radiological features of absent third ventricle: a case series and review of holoprosencephaly spectrum. Pediatr Neurol. 2023.
Blaser SI, Pulver AE. Neuroimaging of developmental brain malformations. In: Barkovich AJ, ed. Pediatric Neuroimaging. 6th ed. Lippincott Williams & Wilkins; 2020.
Medication Comparisons
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This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 26, 2026. · Read our editorial policy