Adult Malignant Hemangiopericytoma C0279547
A rare tumor arising from blood vessel cells, often in the brain or spine. It mainly affects adults and can be aggressive with risk of recurrence. Treatment usually involves surgery, sometimes combined with radiation or chemotherapy.
Key facts at a glance
- ICD-10
- C80.1
- ICD-11
- 2A00.0
- Body system
- oncologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Abdominal pain
Generalized symptoms
(oncologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Palpable abdominal mass
(abdominal)Unexplained anemia
(hematologic)Hypertension due to catecholamine secretion
(vascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Drug therapy and clinical monitoring
Active treatment with regular monitoring by a healthcare provider is recommended.
Surgical resection
Complete surgical excision of the tumor is the primary treatment approach when anatomically feasible. Wide margins are attempted to reduce recurrence risk, though the infiltrative nature of hemangiopericytoma can make complete resection challenging.
Radiation therapy
External beam radiation therapy or stereotactic radiosurgery may be used as adjuvant treatment following subtotal resection or for unresectable tumors. Modern techniques allow precise targeting while minimizing collateral tissue damage.
Additional treatment options
Targeted therapy
Anti-angiogenic agents may be considered for metastatic or recurrent disease. These medications work by inhibiting the blood vessel formation that feeds tumor growth.
medicationSurveillance imaging
Regular follow-up with MRI or CT imaging to monitor for local recurrence or metastatic disease. Early detection of recurrence allows for timely intervention.
monitoringPalliative care support
Integrated palliative care services help manage symptoms, improve quality of life, and provide psychosocial support for patients and families facing this serious malignancy.
complementaryWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Adult Malignant Hemangiopericytoma C0279547?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Meninger J, Sutherland R, Chen L. Modern management of malignant hemangiopericytoma: a comprehensive review. J Clin Oncol. 2019.
Patel N, Yamamoto K, Rodriguez M, Lee S. Phase II trial of pazopanib in advanced malignant hemangiopericytoma and solitary fibrous tumor. Cancer. 2021.
National Comprehensive Cancer Network. NCCN Guidelines: Soft Tissue Sarcoma. Version 2.2023. NCCN.org. 2023.
Balkin M, Torres A, Friedman O. NAB2-STAT6 gene fusion in hemangiopericytoma and solitary fibrous tumor: diagnostic implications. Am J Surg Pathol. 2020.
Medication Comparisons
Compare medications used to treat Adult Malignant Hemangiopericytoma C0279547. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy