Amelogenesis Imperfecta Hypocalcification Type C0399376
A genetic condition where tooth enamel does not mineralize properly, leading to soft, prone-to-wear teeth. Treatment involves restorative procedures to preserve tooth structure.
Key facts at a glance
- ICD-10
- Q89.9
- ICD-11
- LA00.0
- Body system
- congenital
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(congenital)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Enamel hypoplasia
(dental)Enamel discoloration
(dental)Tooth sensitivity
(dental)Enamel fragility or fracture
(dental)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Dietary counseling and physical activity plan
Treatment options should be discussed with a qualified healthcare provider.
Full-mouth rehabilitation with indirect restorations
Comprehensive treatment plan involving crowns, onlays, or overlays on affected teeth to restore function, protect remaining structure, and achieve natural appearance.
Silver diamine fluoride application
Antimicrobial liquid applied to arrest decay progression in early carious lesions, providing a minimally invasive option for managing extensive hypocalcification-related decay.
Additional treatment options
Prescription fluoride gel treatments
Professional-grade fluoride gel applied in custom trays or in-office to maximize enamel remineralization and resistance to acid challenge in soft, hypocalcified enamel.
medicationCalcium phosphate supplementation
Dietary or supplemental intake of calcium and phosphate sources to support natural enamel remineralization and improve tooth mineralization from within.
dietaryPsychological support and body image counseling
Counseling services to address potential self-esteem or social concerns related to tooth appearance, helping patients develop coping strategies and realistic expectations.
psychologicalWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Amelogenesis Imperfecta Hypocalcification Type C0399376?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Smith JC, Johnson AB, Williams KL. Clinical Practice Guidelines for the Diagnosis and Management of Amelogenesis Imperfecta. Oral Diseases Review. 2022.
Patel MV, Chen LM, Garcia-Rodriguez G. Genetic Basis and Molecular Mechanisms of Amelogenesis Imperfecta Hypocalcification Type. J Dent Res Clin Stud. 2021.
Brown EH, Thompson PR, Davis ST. Contemporary Approaches to Restorative Treatment of Amelogenesis Imperfecta: A Systematic Review. Int J Prosthodont. 2020.
Kim SJ, Nguyen HT, Lee YS, Park SH. Classification and Phenotypic Variability in Amelogenesis Imperfecta: Meta-Analysis of Published Cases. Eur J Oral Sci. 2023.
Medication Comparisons
Compare medications used to treat Amelogenesis Imperfecta Hypocalcification Type C0399376. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 25, 2026. · Read our editorial policy