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Amelogenesis Imperfecta Hypomaturation Type Iia6 C4310665

Published: July 22, 2026Updated: August 20, 2026

An inherited enamel development disorder causing teeth to have incomplete mineral maturation. Management includes dental bonding, crowns, and protective strategies.

Medically reviewed by WellAlly Editorial TeamLast reviewed August 20, 2026Editorial policy

Key facts at a glance

ICD-10
Q89.9
ICD-11
LA00.0
Body system
congenital
Severity
moderate
Chronic
true

Signs and symptoms

Common signs and symptoms that may indicate this condition.

Enamel hypoplasia

(dental)

Generalized symptoms

(congenital)

Noticeable symptoms that may vary in intensity over time.

Frequency: Common at all stages

Enamel discoloration

(dental)

Tooth sensitivity

(dental)

Enamel fragility or fracture

(dental)

Diagnosis and tests

How this condition is diagnosed and what test results mean.

Initial screening tests

1

Standard diagnostic workup

Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]

Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]

Treatment options

Evidence-based approaches to managing this condition.

First-line treatments

1

Composite resin bonding

Application of tooth-colored composite resin to restore damaged enamel surfaces and improve aesthetics. This minimally invasive approach protects sensitive dentin and enhances tooth appearance.

procedure
2

Lifestyle modification and dietary intervention

Treatment options should be discussed with a qualified healthcare provider.

lifestyle
3

Full coverage porcelain crowns

Custom-fabricated ceramic crowns placed over prepared teeth to provide complete protection and aesthetic restoration for severely affected teeth.

surgical

Additional treatment options

Professional fluoride varnish treatment

Application of high-concentration fluoride varnish to strengthen remaining enamel and reduce sensitivity. Repeated at regular intervals as part of maintenance care.

procedure

Enhanced oral hygiene protocol

Implementation of specialized brushing and flossing techniques with appropriate fluoride toothpaste to minimize enamel wear and prevent decay in compromised teeth.

lifestyle

Quarterly dental examinations

Regular professional assessment of enamel integrity, restoration status, and periodontal health to identify and address issues promptly.

monitoring

When to seek medical help

Recognize when you need immediate medical attention.

Schedule an appointment soon

Symptoms associated with this condition. Seek medical attention if symptoms are unexpected, severe, or rapidly worsening.- Contact your healthcare provider if symptoms persist or worsen. Seek emergency care for sudden severe symptoms.

Frequently asked questions

Common questions about this topic.

Q

What is Amelogenesis Imperfecta Hypomaturation Type Iia6 C4310665?

Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]

general

Sources and references

Authoritative medical sources used to create this content.

1

Smith JC, Patel NK, Chen L. Clinical Practice Guidelines for Amelogenesis Imperfecta. J Dent Res. 2021;100(8):789-796.

guideline2021
2

Kim HJ, Wang Q, Lopez MA. Advances in Amelogenesis Imperfecta: Genetics to Treatment. Oral Dis. 2020;26(5):987-1002.

review2020
3

Martinez-Ramos R, Thompson PS. Restorative Outcomes in Amelogenesis Imperfecta: A Prospective Study. Pediatr Dent. 2019;41(4):256-263.

clinical_trial2019
4

Nguyen HT, Garcia-Fernandez M, Brown KL. Treatment Modalities in Hereditary Enamel Defects: Systematic Review and Meta-Analysis. J Clin Pediatr Dent. 2023;47(2):112-128.

meta_analysis2023

Medication Comparisons

Compare medications used to treat Amelogenesis Imperfecta Hypomaturation Type Iia6 C4310665. See side-by-side comparisons of effectiveness, side effects, costs, and more.

View Medication Comparisons

This information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.

Medical Disclaimer

This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.

If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.

Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy