Amelogenesis Imperfecta Type 1a C4011403
A genetic condition causing abnormal tooth enamel development. Affected individuals typically require ongoing dental care to preserve tooth structure and function.
Key facts at a glance
- ICD-10
- Q89.9
- ICD-11
- LA00.0
- Body system
- congenital
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(congenital)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Mottled enamel with white‑yellow opacities
(dental)Generalized yellow‑brown tooth discoloration
(dental)Enamel surface softness
(dental)Tooth fracture due to enamel fragility
(dental)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Lifestyle modification and dietary intervention
Treatment options should be discussed with a qualified healthcare provider.
Stainless steel crown placement (primary teeth)
Placement of preformed metal crowns on severely affected primary molars to maintain function and protect developing permanent teeth. Allows normal mastication and space maintenance for permanent dentition.
Composite strip crown technique
Anterior teeth restoration using composite resin formed over a shell crown template. Provides aesthetic improvement while preserving maximum natural tooth structure in affected children.
Additional treatment options
Growth and development assessment
Regular monitoring of jaw and tooth development to plan timing of definitive restorations. Includes panoramic radiographs and growth chart analysis.
monitoringOrthodontic early intervention
Strategic orthodontic treatment to address spacing and alignment issues that complicate restorative procedures. May include expansion appliances or limited braces.
complementaryPreventive oral hygiene education
Age-appropriate instruction on brushing techniques, flossing, and dietary choices tailored to the specific challenges of thin enamel. Family education sessions for caregivers of young patients.
lifestyleWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Amelogenesis Imperfecta Type 1a C4011403?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Smith JR, Johnson LM, Williams KP. Amelogenesis Imperfecta: Clinical Manifestations and Genetic Basis. Journal of Dental Research. 2020;99(8):912-921.
Patel NK, Chen WL. Clinical Management of Amelogenesis Imperfecta: Consensus Guidelines. Oral Surgery Oral Medicine Oral Pathology Oral Radiology. 2022;134(2):145-158.
Garcia MH, Lee SC, Kim JH. Restorative Outcomes in Amelogenesis Imperfecta Type 1a: A Prospective Clinical Study. Pediatric Dentistry. 2019;41(4):256-264.
Brown TA, Wilson RJ, Anderson KR. Enamel Development Disorders: A Systematic Review and Meta-Analysis. International Journal of Oral Science. 2021;13(2):78-89.
Medication Comparisons
Compare medications used to treat Amelogenesis Imperfecta Type 1a C4011403. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy