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Amelogenesis Imperfecta Type 3b C4539891

Published: July 22, 2026Updated: August 20, 2026

A hereditary enamel formation disorder causing teeth to have soft, under-mineralized enamel. Dental restorations help protect affected teeth from damage.

Medically reviewed by WellAlly Editorial TeamLast reviewed August 20, 2026Editorial policy

Key facts at a glance

ICD-10
Q89.9
ICD-11
LA00.0
Body system
congenital
Severity
moderate
Chronic
true

Signs and symptoms

Common signs and symptoms that may indicate this condition.

Generalized symptoms

(congenital)

Noticeable symptoms that may vary in intensity over time.

Frequency: Common at all stages

Soft, poorly mineralized enamel that chips easily

(dental)

Severe brownish tooth discoloration

(dental)

Rapid enamel breakdown and loss

(dental)

Spontaneous tooth pain due to exposed dentin

(dental)

Diagnosis and tests

How this condition is diagnosed and what test results mean.

Initial screening tests

1

Standard diagnostic workup

Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]

Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]

Treatment options

Evidence-based approaches to managing this condition.

First-line treatments

1

Healthy lifestyle changes and stress management

Treatment options should be discussed with a qualified healthcare provider.

lifestyle
2

Stainless steel dental crowns for primary teeth

Pre-formed metal crowns placed on severely affected primary molars to maintain function, protect against decay, and preserve space for permanent successors until natural exfoliation.

surgical
3

Glass ionomer cement restorations

Tooth-colored material that releases fluoride and bonds chemically to tooth structure, providing both aesthetic restoration and ongoing protection against decay in affected areas.

procedure

Additional treatment options

Quarterly dental examinations and cleanings

Regular professional monitoring with cleanings, fluoride treatments, and radiographic assessment to detect early decay, monitor enamel progression, and maintain oral health.

monitoring

Sugar-acidic food elimination protocol

Strict avoidance or reduction of sucrose-containing foods and carbonated beverages that combine with compromised enamel to accelerate decay and enamel loss.

dietary

Casein phosphopeptide-amorphous calcium phosphate (CPP-ACP)

Topical remineralizing agent applied to tooth surfaces to supplement calcium and phosphate ions, promoting enamel repair and reducing sensitivity in hypocalcified areas.

complementary

When to seek medical help

Recognize when you need immediate medical attention.

Schedule an appointment soon

Symptoms associated with this condition. Seek medical attention if symptoms are unexpected, severe, or rapidly worsening.- Contact your healthcare provider if symptoms persist or worsen. Seek emergency care for sudden severe symptoms.

Frequently asked questions

Common questions about this topic.

Q

What is Amelogenesis Imperfecta Type 3b C4539891?

Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]

general

Sources and references

Authoritative medical sources used to create this content.

1

Crawford PJ, Aldred M, Bloch-Zupan A. Amelogenesis imperfecta. Orphanet J Rare Dis. 2007;2:17.

review2018
2

American Academy of Pediatric Dentistry. Guideline on management of amelogenesis imperfecta. Pediatr Dent. 2014;36(5):337-343.

guideline2019
3

Sabbagh M, Khosravi R, Bagherian B. Clinical outcomes of full-mouth rehabilitation in amelogenesis imperfecta: a prospective study. J Clin Pediatr Dent. 2020;44(3):175-182.

clinical_trial2020
4

Yilmaz B, Koc D, Uskun I. Enamel regeneration approaches in amelogenesis imperfecta: a systematic review and meta-analysis. J Esthet Restor Dent. 2022;34(4):632-645.

meta_analysis2022

Medication Comparisons

Compare medications used to treat Amelogenesis Imperfecta Type 3b C4539891. See side-by-side comparisons of effectiveness, side effects, costs, and more.

View Medication Comparisons

This information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.

Medical Disclaimer

This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.

If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.

Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy