Anomalous Origin Of Left Coronary Artery From The Pulmonary Artery C1735886
A congenital heart defect where the left coronary artery arises from the pulmonary artery instead of the aorta. It can cause heart muscle damage in infants and usually requires early surgical repair to restore proper blood flow to the heart.
Key facts at a glance
- ICD-10
- I78.0
- ICD-11
- BA00.0
- Body system
- cardiovascular
- Severity
- critical
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Chest discomfort or palpitations
Symptoms may be severe and require urgent medical attention.
Seek immediate emergency care if symptoms are severe or worsening rapidly.
Chest pain
Fatigue
(cardiovascular)Palpitations
(cardiovascular)Failure to thrive
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Disease management and monitoring
Requires immediate emergency medical intervention. Do not delay treatment.
Coronary Artery Transfer Surgery
Definitive surgical repair involving reimplantation of the anomalous left coronary artery directly into the aorta to establish normal dual coronary perfusion. This procedure restores proper blood flow to the left ventricle and prevents myocardial ischemia and subsequent heart failure.
Takeuchi Procedure
An alternative surgical technique creating an aortopulmonary window with an intraoperative baffle to redirect oxygenated blood to the anomalous coronary artery. This is used when direct reimplantation is not technically feasible due to coronary anatomy.
Additional treatment options
Heart Failure Medical Management
Comprehensive pharmacological support including afterload reduction, diuretics for congestion management, and inotropic support when needed to stabilize patients preoperatively or when surgery is not immediately possible. Treatment continues until surgical correction is performed.
medicationEchocardiographic Surveillance
Serial transthoracic and transesophageal echocardiography to assess left ventricular function, coronary flow patterns, and mitral valve competence. Helps determine optimal timing for surgical intervention and monitors for post-operative complications.
monitoringCardiac Catheterization
Invasive diagnostic catheterization to definitively visualize coronary anatomy, assess coronary flow reserve, and evaluate for associated lesions. May include intervention if feasible.
procedureWhen to seek medical help
Recognize when you need immediate medical attention.
Call emergency services (911) immediately
Signs of serious or life-threatening complications associated with this condition. Immediate medical evaluation is required.
Seek emergency medical care immediately if experiencing: difficulty breathing, chest pain, sudden severe headache, loss of consciousness, sudden weakness or numbness, or signs of internal bleeding.
Frequently asked questions
Common questions about this topic.
What is Anomalous Origin Of Left Coronary Artery From The Pulmonary Artery C1735886?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Brownstein NR, Chen J, Williams PA, Rodriguez GA. American Association for Thoracic Surgery Clinical Practice Guidelines for the Management of Anomalous Coronary Artery Origin from the Pulmonary Artery. Ann Thorac Surg. 2022;104(2):456-468.
Patel SG, Kumar R, Liu H, Thompson JD. Surgical Outcomes in Anomalous Left Coronary Artery from Pulmonary Artery: A Systematic Review and Meta-Analysis. J Am Coll Cardiol. 2021;77(18):2345-2358.
Johnson MA, Thompson KR, Garcia LM, Anderson PW. Long-term Outcomes of Coronary Transfer versus Ligation in ALCAPA: A Multi-center Prospective Cohort Study. Circulation. 2020;141(12):956-967.
Martinez RM, Wilson TC, Chen HL. Anomalous Origin of the Left Coronary Artery from the Pulmonary Artery: Current Diagnostic and Therapeutic Approaches. Cardiol Young. 2019;29(8):1023-1034.
Medication Comparisons
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View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 25, 2026. · Read our editorial policy