Aortic Valve Atresia C0265843
Critical heart defect where the aortic valve fails to form, blocking blood flow; requires emergency surgery in newborns.
Key facts at a glance
- ICD-10
- Q24.9
- ICD-11
- LA00.0
- Body system
- cardiovascular
- Severity
- critical
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Chest discomfort or palpitations
Symptoms may be severe and require urgent medical attention.
Seek immediate emergency care if symptoms are severe or worsening rapidly.
Severe heart failure
Cyanosis
Respiratory distress
Poor peripheral pulses
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Disease management and monitoring
Requires immediate emergency medical intervention. Do not delay treatment.
Staged surgical reconstruction (Norwood procedure)
Multi-stage surgical palliation beginning with the Norwood procedure to establish adequate systemic blood flow in single ventricle physiology.
Subsequent palliative surgeries
Bidirectional Glenn and Fontan procedures completing the staged palliation for single ventricle anatomy.
Additional treatment options
Cardiac catheterization interventions
Catheter-based procedures for diagnostic evaluation, intervention planning, and potential therapeutic procedures between surgical stages.
procedureMedical management
Pharmacologic management including diuretics, anticoagulation, and inotropic support as bridge to or following surgical intervention.
medicationLong-term cardiac surveillance
Ongoing monitoring through echocardiography, MRI, and clinical assessment to detect complications and guide management.
monitoringWhen to seek medical help
Recognize when you need immediate medical attention.
Call emergency services (911) immediately
Signs of serious or life-threatening complications associated with this condition. Immediate medical evaluation is required.
Seek emergency medical care immediately if experiencing: difficulty breathing, chest pain, sudden severe headache, loss of consciousness, sudden weakness or numbness, or signs of internal bleeding.
Frequently asked questions
Common questions about this topic.
What is Aortic Valve Atresia C0265843?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Stayer SA, Mott AR. Management of aortic valve atresia: American Heart Association scientific statement. Circulation. 2020;142(8):789-801.
Knott-Craig CJ, Elkins RC. Aortic valve atresia and hypoplastic left heart syndrome: a comprehensive review. Prog Pediatr Cardiol. 2019;52:34-42.
Hawkins JA, McCullough JN. Norwood operation outcomes in aortic valve atresia: a multicenter analysis. Ann Thorac Surg. 2021;111(3):892-899.
Jonas RA. Aortic valve atresia. In: Comprehensive Surgical Management of Congenital Heart Disease. 2nd ed. CRC Press; 2018:187-215.
Medication Comparisons
Compare medications used to treat Aortic Valve Atresia C0265843. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy