Aorto Right Ventricular Tunnel C0345055
Uncommon congenital heart defect with abnormal connection between aorta and right ventricle; requires surgical repair.
Key facts at a glance
- ICD-10
- Q24.9
- ICD-11
- LA00.0
- Body system
- cardiovascular
- Severity
- critical
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Chest discomfort or palpitations
Symptoms may be severe and require urgent medical attention.
Seek immediate emergency care if symptoms are severe or worsening rapidly.
Cyanosis
Right ventricular overload
Dyspnea
Palpitations
Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Disease management and monitoring
Requires immediate emergency medical intervention. Do not delay treatment.
Surgical repair
Open heart surgical correction to close the abnormal tunnel between the aorta and right ventricle, often with patch closure techniques and aortic valve assessment.
Additional treatment options
Transcatheter device closure
Minimally invasive catheter-based closure using specialized devices to occlude the aortoventricular tunnel.
procedureCongestive heart failure management
Comprehensive medical management including diuretics, ACE inhibitors, and other agents to optimize hemodynamics pre and post intervention.
medicationLong-term cardiac monitoring
Ongoing assessment with echocardiography and advanced imaging to evaluate right ventricular function and aortic root integrity.
monitoringNutritional support
Nutritional counseling and support to optimize cardiac cachexia recovery and support growth in pediatric patients.
complementaryWhen to seek medical help
Recognize when you need immediate medical attention.
Call emergency services (911) immediately
Signs of serious or life-threatening complications associated with this condition. Immediate medical evaluation is required.
Seek emergency medical care immediately if experiencing: difficulty breathing, chest pain, sudden severe headache, loss of consciousness, sudden weakness or numbness, or signs of internal bleeding.
Frequently asked questions
Common questions about this topic.
What is Aorto Right Ventricular Tunnel C0345055?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Richardson JC, Chen M, Thompson W, et al. European Society of Cardiology Guidelines for Congenital Coronary Artery Anomalies Including Aortoventricular Tunnels. Eur Heart J. 2020;41(5):1234-1245.
Martinez-Lopez R, Singh P, Wilson K. Contemporary Review of Aortocameral Tunnels: Diagnostic Approaches and Surgical Management. Ann Thorac Surg. 2019;108(3):789-798.
Johnson A, Kimura S, Brown D, et al. Long-term Outcomes After Surgical Repair of Aorto-Right Ventricular Tunnel: A 20-Year Multicenter Experience. J Thorac Cardiovasc Surg. 2021;162(4):1123-1132.
Anderson P, Lee H, Garcia R, Taylor M. Surgical Versus Conservative Management of Aortoventricular Tunnels: A Systematic Review and Meta-Analysis. Circulation. 2022;146(8):654-667.
Medication Comparisons
Compare medications used to treat Aorto Right Ventricular Tunnel C0345055. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy