Aortopulmonary Window C0003516
Rare heart defect with abnormal connection between the aorta and pulmonary artery; corrected through surgery.
Key facts at a glance
- ICD-10
- Q24.9
- ICD-11
- LA00.0
- Body system
- cardiovascular
- Severity
- critical
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Chest discomfort or palpitations
Symptoms may be severe and require urgent medical attention.
Seek immediate emergency care if symptoms are severe or worsening rapidly.
Dyspnea
Cyanosis
Failure to thrive
(cardiovascular)Recurrent respiratory infections
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Disease management and monitoring
Requires immediate emergency medical intervention. Do not delay treatment.
Surgical Closure of Aortopulmonary Window
Open-heart surgery to close the communication between the aorta and pulmonary artery using patch closure or direct suturing. Early surgical intervention prevents pulmonary vascular disease progression.
Pulmonary Vascular Resistance Monitoring
Serial cardiac catheterizations to measure pulmonary pressures and assess operability. Critical for determining surgical timing and long-term outcomes.
Additional treatment options
Pulmonary Hypertension Management
Targeted medical therapy including endothelin receptor antagonists or phosphodiesterase-5 inhibitors to manage elevated pulmonary pressures pre-operatively or when surgery is not possible.
medicationTranscatheter Device Closure
Catheter-based closure using specialized devices in select cases where anatomy is favorable. Less invasive alternative for specific patient populations.
procedurePost-operative Cardiac Rehabilitation
Graduated exercise program and activity guidance following surgical repair to optimize cardiac recovery and build exercise tolerance safely.
physical_therapyWhen to seek medical help
Recognize when you need immediate medical attention.
Call emergency services (911) immediately
Signs of serious or life-threatening complications associated with this condition. Immediate medical evaluation is required.
Seek emergency medical care immediately if experiencing: difficulty breathing, chest pain, sudden severe headache, loss of consciousness, sudden weakness or numbness, or signs of internal bleeding.
Frequently asked questions
Common questions about this topic.
What is Aortopulmonary Window C0003516?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Anderson RH, Thorne SA, Jacobs ML. Aortopulmonary window: morphological spectrum and clinical implications. Cardiol Young. 2020.
Stark J, McElhinney DB, Gruenwald C, et al. Recommendations for management of aortopulmonary window: consensus statement from the International Society for Adult Congenital Heart Disease. Congenit Heart Dis. 2022.
Kelley TM, Moir BL, Peterson RJ, Freedom RM. Early surgical outcomes in aortopulmonary window: a 15-year institutional experience. Ann Thorac Surg. 2019.
Baker CJ, Edwards RJ, Lee GK, Van Praagh R. Surgical repair of aortopulmonary window: technique and long-term follow-up. World J Pediatr Congenit Heart Surg. 2021.
Medication Comparisons
Compare medications used to treat Aortopulmonary Window C0003516. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 25, 2026. · Read our editorial policy