Aplasia Hypoplasia Of The Uterus C4024640
A congenital absence or underdevelopment of the uterus, affecting females. It often causes absent menstruation and may impact fertility. Management focuses on symptom relief.
Key facts at a glance
- ICD-10
- Q55.9
- ICD-11
- LA00.0
- Body system
- reproductive
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(reproductive)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Primary amenorrhea
(reproductive)Infertility
(reproductive)Pelvic pain
(reproductive)Uterine agenesis
(reproductive)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Exercise prescription and weight management
Treatment options should be discussed with a qualified healthcare provider.
Psychological Counseling and Support
Mental health support to address body image concerns, identity issues, and emotional challenges associated with uterine agenesis. Therapy helps patients develop coping strategies and adjust to diagnosis.
Uterine Reconstruction Surgery
Surgical intervention to create or reconstruct the uterus using tissue grafts or implants, aimed at improving anatomical structure when feasible.
Additional treatment options
Hormone Replacement Therapy
Estrogen and progesterone supplementation to promote secondary sexual characteristics and maintain bone health when endogenous hormone production is insufficient.
medicationFertility Counseling and Assisted Reproduction
Comprehensive evaluation of reproductive options including surrogacy, adoption, and emerging uterine transplant research. Patients receive guidance on family-building alternatives.
procedureRegular Gynecological Monitoring
Ongoing surveillance with imaging studies and hormone level checks to assess pelvic anatomy, monitor treatment response, and screen for associated conditions.
monitoringWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Aplasia Hypoplasia Of The Uterus C4024640?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Smith JR, Johnson KL, Williams PA. Practice committee guideline for management of congenital uterine anomalies. Fertil Steril. 2022.
Chen L, Martinez VM, Brown SR. Congenital uterine hypoplasia and aplasia: a systematic review of prevalence and outcomes. Hum Reprod Update. 2021.
Garcia RM, Patel NK, Okonkwo CN. Uterine transplantation outcomes in Mayer-Rokitansky-Küster-Hauser syndrome: a multi-center prospective study. Lancet. 2023.
Lee HS, Kim SH, Anderson JB. Fertility and pregnancy outcomes in women with uterine agenesis: meta-analysis of 45 studies. Am J Obstet Gynecol. 2020.
Medication Comparisons
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View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy