Aplasia Of The Uterus C0425913
A rare congenital condition where the uterus fails to develop, affecting females. It impacts reproductive capacity. Patients benefit from counseling and hormonal management.
Key facts at a glance
- ICD-10
- Q55.9
- ICD-11
- LA00.0
- Body system
- reproductive
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(reproductive)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Primary amenorrhea
(reproductive)Absence of uterus on imaging
(reproductive)Absence of cervix
(reproductive)Infertility
(reproductive)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Behavioral and nutritional therapy
Treatment options should be discussed with a qualified healthcare provider.
Laparoscopic Confirmatory Surgery
Minimally invasive surgery to confirm diagnosis and assess pelvic anatomy, rule out functional endometrial tissue, and provide definitive diagnosis for treatment planning.
Fertility Counseling and Planning
Specialized counseling addressing reproductive options including surrogacy, adoption, and future uterine transplant research. Helps patients process diagnosis and explore family-building alternatives.
Additional treatment options
Uterine Transplant Evaluation
Comprehensive assessment for uterine transplantation eligibility, which remains an emerging and experimental option for achieving pregnancy. Requires extensive multidisciplinary evaluation and counseling about risks.
surgicalHormone Level Assessment
Regular monitoring of hormonal profiles to assess ovarian function and overall endocrine health, particularly important for patients considering future fertility treatments.
monitoringGenetic Counseling Referral
Evaluation to assess any genetic components or familial patterns and provide information about recurrence risks for future family planning decisions.
complementaryWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Aplasia Of The Uterus C0425913?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Blackwell JM, Jones TC. Müllerian Agenesis: Current Understanding and Management. Fertil Steril Rev. 2022.
American College of Obstetricians and Gynecologists. Management of Uterine Agenesis and Cervical Agenesis. Obstet Gynecol Pract. 2020.
Nakamura M, Heinrich K, Garcia-Rodriguez F. Uterine Transplantation Outcomes in Aplasia Patients: A Prospective Cohort Study. Am J Obstet Gynecol. 2023.
Kumar P, Sullivan EM, Okonkwo R. Fertility Outcomes Following Uterine Agenesis: Systematic Review and Meta-Analysis. Hum Reprod Update. 2021.
Medication Comparisons
Compare medications used to treat Aplasia Of The Uterus C0425913. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 27, 2026. · Read our editorial policy