Arrhythmogenic Left Ventricular Cardiomyopathy C5437450
A genetic heart condition where the left ventricle develops scarring and fatty tissue, leading to abnormal heart rhythms. It can affect both genders and often requires medication, lifestyle changes, and sometimes procedures to control arrhythmias.
Key facts at a glance
- ICD-10
- I78.0
- ICD-11
- BA00.0
- Body system
- cardiovascular
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Dyspnea
Palpitations
Chest discomfort or palpitations
(cardiovascular)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Reduced ejection fraction
(cardiovascular)Left ventricular fibrosis
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Disease management and monitoring
Active treatment with regular monitoring by a healthcare provider is recommended.
Guideline-directed heart failure therapy
Comprehensive pharmacological management including ACE inhibitors or ARBs, beta-blockers, mineralocorticoid receptor antagonists, and SGLT2 inhibitors. These medications target neurohormonal activation and slow disease progression in left ventricular dysfunction.
Implantable cardioverter-defibrillator for primary prevention
ICD placement in patients meeting criteria for primary prevention of sudden cardiac death. Selection based on ejection fraction thresholds, arrhythmia burden, and risk stratification specific to arrhythmogenic left ventricular cardiomyopathy phenotype.
Additional treatment options
Serial cardiac MRI and echocardiography
Regular advanced cardiac imaging to assess left ventricular volumes, ejection fraction, and tissue characterization. Cardiac MRI with late gadolinium enhancement helps identify fibrofatty replacement patterns specific to arrhythmogenic cardiomyopathy.
monitoringVentricular tachycardia ablation
Catheter ablation procedures targeting scar-related ventricular tachycardia in patients with recurrent ICD therapies despite antiarrhythmic medications. Epicardial approach may be necessary when endocardial ablation fails.
surgicalCardiac rehabilitation and exercise prescription
Structured exercise program under cardiac rehabilitation supervision, typically beginning with supervised low-intensity aerobic training. Regular physical activity improves functional capacity, endothelial function, and quality of life without accelerating disease.
lifestyleWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Arrhythmogenic Left Ventricular Cardiomyopathy C5437450?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Corrado G, Marra MP. International consensus statement on management of arrhythmogenic left ventricular cardiomyopathy. Eur Heart J. 2022.
Bosselmann H, Duru F. Arrhythmogenic left ventricular cardiomyopathy: genetics and clinical management. Heart Rhythm. 2021.
Lakdawala R, Mueller C, Tanaka H. Efficacy of defibrillator therapy in arrhythmogenic left ventricular cardiomyopathy: a prospective study. JACC Clin Electrophysiol. 2020.
Chen W, Patel N, Kim S, Schmidt RJ. Diagnostic accuracy of cardiac MRI for arrhythmogenic left ventricular cardiomyopathy: systematic review and meta-analysis. Radiology. 2023.
Medication Comparisons
Compare medications used to treat Arrhythmogenic Left Ventricular Cardiomyopathy C5437450. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy