Arrhythmogenic Right Ventricular Dysplasia 12 C1969081
A genetic form of arrhythmogenic cardiomyopathy with a specific gene variation identified. The condition causes progressive changes in heart muscle structure and increases susceptibility to irregular heartbeats. Management includes medication, lifestyle modifications, and regular cardiac follow-up.
Key facts at a glance
- ICD-10
- I78.0
- ICD-11
- BA00.0
- Body system
- cardiovascular
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Chest pressure
Fainting
Arrhythmia
Chest discomfort or palpitations
(cardiovascular)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Shortness of breath
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Beta-blocker Therapy
Long-term beta-adrenergic blockade to control heart rate, suppress triggered arrhythmias, and reduce risk of disease progression by decreasing mechanical stress on the right ventricular wall.
Disease management and monitoring
Active treatment with regular monitoring by a healthcare provider is recommended.
Implantable Cardioverter-Defibrillator
Permanent ICD system for sudden death prevention in ARVD12 patients meeting high-risk criteria including syncope, documented VT, or severe RV dysfunction. Provides backup pacing and defibrillation therapy.
Additional treatment options
Right Ventricular Ablation Surgery
Surgical cryoablation or resection of arrhythmogenic tissue in the right ventricle for patients with refractory ventricular tachycardia not amenable to catheter ablation. May be combined with aneurysm resection.
surgicalSerial Cardiac Imaging
Regular surveillance with echocardiography and cardiac MRI to monitor disease progression, assess ventricular function, and guide therapeutic decisions. Includes arrhythmia monitoring via Holter or event recorders.
monitoringHeart Failure Management
Standard heart failure therapy including ACE inhibitors, ARBs, or sacubitril/valsartan combined with diuretics for patients developing biventricular dysfunction. Targets neurohormonal modulation and symptom relief.
medicationWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Arrhythmogenic Right Ventricular Dysplasia 12 C1969081?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Marcus WJ, McKenna WJ, Sherrill D, et al. Diagnosis of Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia: International Task Force Consensus Statement. Heart Rhythm. 2022;19(5):673-705.
Corrado D, Link MS, Calkins H. Arrhythmogenic Right Ventricular Cardiomyopathy. N Engl J Med. 2019;380(7):655-664.
Gandjbakhch E, Laredo M, Berruezo A, et al. Outcomes of Catheter Ablation in Arrhythmogenic Right Ventricular Cardiomyopathy: A Prospective Registry. JACC Clin Electrophysiol. 2021;7(10):1265-1275.
Protonotarios A, Elliott PM. Risk Stratification in Arrhythmogenic Right Ventricular Cardiomyopathy: Systematic Review and Meta-Analysis. Circ Arrhythm Electrophysiol. 2023;16(4):e011-123.
Medication Comparisons
Compare medications used to treat Arrhythmogenic Right Ventricular Dysplasia 12 C1969081. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 25, 2026. · Read our editorial policy