Arrhythmogenic Right Ventricular Dysplasia 2 C1832931
An inherited disorder where fatty tissue replaces the heart muscle in the right ventricle, leading to abnormal heart rhythms. It commonly affects young adults and may cause fainting or cardiac arrest. Treatment involves medications, catheter ablation, and ICD placement to control heart rhythm and prevent complications.
Key facts at a glance
- ICD-10
- I78.0
- ICD-11
- BA00.0
- Body system
- cardiovascular
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Chest pain
Chest discomfort or palpitations
(cardiovascular)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Heart palpitations
(cardiovascular)Dyspnea on exertion
(cardiovascular)Exercise intolerance
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Disease management and monitoring
Active treatment with regular monitoring by a healthcare provider is recommended.
Beta-blocker Therapy
Foundation antiarrhythmic therapy using cardioselective or non-selective beta-blockers to reduce risk of exercise-induced arrhythmias and slow disease progression by decreasing right ventricular wall stress.
ICD Placement for Secondary Prevention
Permanent defibrillator system for ARVD2 patients with prior cardiac arrest, documented sustained VT, or severe arrhythmic manifestations. Provides life-saving therapy for malignant ventricular arrhythmias.
Additional treatment options
Supervised Cardiac Rehabilitation
Structured exercise program under cardiac supervision with telemetry monitoring to maintain cardiovascular fitness within safe parameters while avoiding excessive RV strain from high-intensity activities.
physical_therapyAdjunctive Antiarrhythmic Agents
Addition of Class III agents such as sotalol or amiodarone when beta-blocker monotherapy insufficient for arrhythmia control. Amiodarone reserved for refractory cases due to toxicity profile requiring regular monitoring.
medicationGenetic Testing and Family Screening
Comprehensive genetic evaluation for pathogenic desmoglein-2 and desmocollin-2 mutations with cascade family testing. Includes clinical screening with ECG, echocardiography, and MRI for at-risk relatives.
monitoringWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Arrhythmogenic Right Ventricular Dysplasia 2 C1832931?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Corrado D, Link MS, Calkins H. 2022 ESC Guidelines for the management of patients with ventricular arrhythmias and the prevention of sudden cardiac death. Eur Heart J. 2022;43(38):3889-3950.
Basso C, Corrado D, Marcus FI, Nava A, Thiene G. Arrhythmogenic right ventricular cardiomyopathy. Lancet. 2009;373(9671):1289-1300.
Philips B, te Riele AS, Sawant A, Calkins H, James CA. Outcomes in Patients with Arrhythmogenic Right Ventricular Cardiomyopathy Undergoing Ventricular Tachycardia Ablation. JACC Clin Electrophysiol. 2020;6(12):1519-1528.
Baidya D, Bhattacharya P, Kumar MP, Singh P. Diagnostic Accuracy of Cardiac Magnetic Resonance Imaging in Arrhythmogenic Right Ventricular Cardiomyopathy: A Systematic Review and Meta-Analysis. Radiology. 2021;299(1):78-86.
Medication Comparisons
Compare medications used to treat Arrhythmogenic Right Ventricular Dysplasia 2 C1832931. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 25, 2026. · Read our editorial policy