Arrhythmogenic Right Ventricular Dysplasia 8 C1843896
A rare genetic disorder causing the heart's right ventricle to weaken as muscle is replaced by fat, leading to arrhythmias and potential sudden death. It often runs in families and affects young adults. Management includes medications, ablation, and ICD placement to control heart rhythm.
Key facts at a glance
- ICD-10
- I78.0
- ICD-11
- BA00.0
- Body system
- cardiovascular
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Chest pain
Ventricular tachycardia
Chest discomfort or palpitations
(cardiovascular)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Palpitations
(cardiovascular)Dyspnea on exertion
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Beta-blocker therapy
Beta-adrenergic blocking agents are used to reduce heart rate, decrease myocardial oxygen demand, and prevent catecholamine-triggered ventricular arrhythmias in ARVD patients.
Disease management and monitoring
Active treatment with regular monitoring by a healthcare provider is recommended.
Implantable cardioverter-defibrillator (ICD)
ICD placement provides continuous monitoring and automatic defibrillation for life-threatening ventricular arrhythmias, serving as primary or secondary prevention in high-risk ARVD patients.
Additional treatment options
Exercise restriction
Structured avoidance of competitive and high-intensity sports to reduce arrhythmia triggers and disease progression risk, replacing with low-intensity recreational activities.
lifestyleCatheter ablation
Radiofrequency catheter ablation targets and eliminates arrhythmogenic foci within the right ventricle, particularly useful for recurrent ventricular tachycardia not controlled by medications.
procedureRegular cardiac surveillance
Periodic echocardiography, cardiac MRI, and Holter monitoring to assess disease progression, ventricular function, and arrhythmia burden for treatment optimization.
monitoringWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Arrhythmogenic Right Ventricular Dysplasia 8 C1843896?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Corrado D, Perazzolo Marra M, Zorzi A, et al. Diagnosis of arrhythmogenic right ventricular cardiomyopathy: 2020 International Task Force Consensus Guidelines. Heart Rhythm. 2020;17(8):1421-1435.
Basso C, Corrado D, Marcus FI, Nava A, Thiene G. Arrhythmogenic right ventricular cardiomyopathy. Lancet. 2009;373(9671):1289-1300.
Wichter T, Paul TM, Eckardt L, Breithardt G, Schulze-Bahr E. Arrhythmogenic right ventricular cardiomyopathy: predictors of ventricular tachycardia and mortality. J Cardiovasc Electrophysiol. 2012;23(5):484-492.
Piccini JP, Dalal D, Tichnell C, Calkins H. Ablation of ventricular tachycardia in arrhythmogenic right ventricular dysplasia/cardiomyopathy: a systematic review. Circ Arrhythm Electrophysiol. 2015;8(6):1403-1410.
Medication Comparisons
Compare medications used to treat Arrhythmogenic Right Ventricular Dysplasia 8 C1843896. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 25, 2026. · Read our editorial policy