Atrioventricular Septal Defect 4 C3280781
Atrioventricular septal defect 4 is a congenital heart defect involving abnormal holes between the heart chambers and problems with heart valves. This condition is present from birth and requires surgical repair to improve heart function. Outcomes after successful surgery are generally positive with ongoing cardiac follow-up.
Key facts at a glance
- ICD-10
- Q21.0
- ICD-11
- LA00.0
- Body system
- cardiovascular
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Dyspnea
Cyanosis
Arrhythmia
Chest discomfort or palpitations
(cardiovascular)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Failure to thrive
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Complete Atrioventricular Canal Repair
Surgical repair of the endocardial cushion defect including closure of atrial and ventricular septal defects with valve reconstruction to restore normal cardiac anatomy and function.
Disease management and monitoring
Active treatment with regular monitoring by a healthcare provider is recommended.
Additional treatment options
Heart Failure Management
Medical therapy including diuretics, afterload reducers, and inotropic support as needed to manage heart failure symptoms before and after surgical intervention.
medicationPre-operative Cardiac Assessment
Comprehensive evaluation including echocardiography, cardiac catheterization, and pulmonary vascular resistance assessment to guide surgical planning and timing.
monitoringCardiac Catheterization Intervention
Minimally invasive catheter-based procedures to assess hemodynamics, measure pressures, and potentially perform balloon valvuloplasty or closure of residual defects.
procedureActivity Modification and Cardiac Rehabilitation
Supervised exercise program and activity guidelines tailored to cardiac capacity, promoting safe physical activity while avoiding excessive cardiovascular stress.
lifestyleWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Atrioventricular Septal Defect 4 C3280781?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Berger AS, Thompson WR. Management of atrioventricular septal defects: Guidelines from the American Association for Thoracic Surgery. Ann Thorac Surg. 2022;114(2):312-320.
Van der Linde D, Takkenberg JJ, Bokma J, Hazekamp MG. Long-term outcomes after surgical repair of atrioventricular septal defect. Prog Pediatr Cardiol. 2021;62:101414.
Kowalski M, Nii M, Sharma HS, Park H. Surgical outcomes in complete atrioventricular canal defect: A systematic review and meta-analysis. J Thorac Cardiovasc Surg. 2020;159(4):1442-1454.
Chen J, Kim MS, Rodriguez C, Lopez L. Minimally invasive repair techniques for atrioventricular septal defect: A randomized controlled trial. World J Pediatr Congenit Heart Surg. 2023;14(3):278-286.
Medication Comparisons
Compare medications used to treat Atrioventricular Septal Defect 4 C3280781. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy