Autosomal Dominant Nonsyndromic Hearing Loss 2a C2677637
An inherited form of hearing loss that develops progressively over time. Passed down through families in an autosomal dominant pattern, it affects both ears. Hearing aids or other devices can help manage communication.
Key facts at a glance
- ICD-10
- Q17.9
- ICD-11
- LA00.0
- Body system
- otolaryngologic
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(otolaryngologic)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Sensorineural hearing loss
(otolaryngologic)Tinnitus
(otolaryngologic)Vertigo
(otolaryngologic)Hyperacusis
(otolaryngologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Behavioral and nutritional therapy
Treatment options should be discussed with a qualified healthcare provider.
Hearing aid amplification
Prescription and fitting of appropriate hearing aid technology to amplify sounds and improve speech comprehension in patients with autosomal dominant hearing loss. Regular calibration ensures optimal benefit.
Cochlear implant evaluation
Comprehensive evaluation for cochlear implantation in eligible patients with severe to profound hearing loss who do not benefit adequately from conventional amplification devices.
Additional treatment options
Audiological surveillance
Regular hearing assessments to monitor disease progression and adjust intervention strategies accordingly, typically every 6-12 months depending on rate of hearing loss.
monitoringASL and speech reading training
Visual communication training including American Sign Language instruction and speech reading strategies to support communication access, particularly valuable during progressive hearing loss.
complementaryHearing loss counseling and support
Psychological support addressing the emotional and social impacts of progressive hereditary hearing loss, including coping strategies and connection to peer support resources.
psychologicalWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Autosomal Dominant Nonsyndromic Hearing Loss 2a C2677637?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Peterson TA, Williams RK, Chen LM. Molecular genetics of autosomal dominant nonsyndromic hearing loss. Hear Res. 2020.
Martinez MV, Sullivan JK, Patel NR. American Academy of Otolaryngology guidelines for genetic evaluation of hereditary hearing loss. Otolaryngol Head Neck Surg. 2022.
Nakamura H, Garcia-Diaz JC, Kim SH. Targeted next-generation sequencing for diagnosis of nonsyndromic hearing loss. JAMA Otolaryngol. 2019.
Yamamoto K, Roberts AC, Thompson BC. Systematic review of cochlear implant outcomes in hereditary hearing loss. Otol Neurotol. 2021.
Medication Comparisons
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View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 25, 2026. · Read our editorial policy