Autosomal Dominant Nonsyndromic Hearing Loss 4a C1833503
A genetic hearing loss passed down through autosomal dominant inheritance. Affects males and females equally. Sound amplification devices and communication therapy help manage the condition.
Key facts at a glance
- ICD-10
- Q17.9
- ICD-11
- LA00.0
- Body system
- otolaryngologic
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(otolaryngologic)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Sensorineural hearing loss
(otolaryngologic)Tinnitus
(otolaryngologic)Vertigo
(otolaryngologic)Hyperacusis
(otolaryngologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Exercise prescription and weight management
Treatment options should be discussed with a qualified healthcare provider.
Hearing Aid Amplification
Prescription hearing aids calibrated to individual audiometric findings to amplify sounds and improve speech comprehension in daily communication.
Cochlear Implantation
Surgical placement of a cochlear implant device that directly stimulates the auditory nerve, bypassing damaged hair cells in the cochlea to restore hearing perception.
Additional treatment options
Assistive Listening Devices
Personal amplifiers, FM systems, and alerting devices that enhance sound transmission in specific listening situations like classrooms or meetings.
complementaryRegular Audiological Monitoring
Serial audiometric assessments and hearing evaluations to track disease progression and adjust intervention strategies accordingly.
monitoringAuditory Rehabilitation Therapy
Structured speech-language therapy focusing on auditory training, lip-reading skills, and communication strategies to maximize residual hearing.
physical_therapyWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Autosomal Dominant Nonsyndromic Hearing Loss 4a C1833503?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Shearer AE, Hildebrand MS, Smith RJ. Hereditary hearing loss and deafness: an update. Clin Genet. 2013.
Alford RL, Arnos KS, Fox M, et al. American College of Medical Genetics and Genomics guideline for the evaluation of nonsyndromic hearing loss and deafness. Genet Med. 2014.
Lalani SR, Sathiamoorthy T, Lee K, et al. Autosomal dominant nonsyndromic hearing loss: phenotype-genotype correlation in families linked to DFNA loci. Mol Syndromol. 2015.
Chen G, Li X, Wang Y, Liu J. Meta-analysis of genetic variants associated with nonsyndromic autosomal dominant hearing loss. JAMA Otolaryngol Head Neck Surg. 2019.
Medication Comparisons
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View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy