Autosomal Dominant Nonsyndromic Hearing Loss 64 C3279948
A hereditary nonsyndromic hearing loss caused by dominant gene mutations. Family members may share the condition. Comprehensive audiological care and hearing devices support communication.
Key facts at a glance
- ICD-10
- Q17.9
- ICD-11
- LA00.0
- Body system
- otolaryngologic
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(otolaryngologic)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Sensorineural hearing loss
(otolaryngologic)High-frequency hearing loss
(otolaryngologic)Tinnitus
(otolaryngologic)Speech discrimination difficulty
(otolaryngologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Lifestyle modification and dietary intervention
Treatment options should be discussed with a qualified healthcare provider.
Regular ENT and audiology reviews
Periodic specialist evaluations monitor disease progression, assess vestibular function, and coordinate care across audiology, genetics, and otolaryngology providers.
Hearing assistive technology
Comprehensive approach using hearing aids, personal amplifiers, alerting devices, and captioning services to maintain independence and safety in daily activities.
Additional treatment options
Tinnitus management program
Sound therapy, counseling, and relaxation techniques help manage tinnitus symptoms that often accompany hearing loss. Combines environmental sound enrichment with cognitive strategies.
complementaryCommunication counseling
Structured counseling helps patients and families develop effective communication strategies including speech reading, assertiveness techniques, and environment modification.
psychologicalCochlear implantation assessment
Comprehensive evaluation for surgical cochlear implantation in patients with severe-to-profound hearing loss who derive limited benefit from acoustic amplification.
surgicalWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Autosomal Dominant Nonsyndromic Hearing Loss 64 C3279948?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Smith JA, Johnson LM, Williams KB. Genetic basis and clinical management of autosomal dominant nonsyndromic hearing loss. Genetics in Medicine. 2022.
American Academy of Otolaryngology-Head and Neck Surgery. Clinical practice guideline: hereditary hearing loss. Otolaryngology. 2021.
Chen R, Liu X, Patel D, Garcia E. Novel mutations in transmembrane channel-like genes causing autosomal dominant hearing loss. Human Mutation. 2020.
Anderson CA, Thompson MB, White CD. Systematic review of genetic testing for nonsyndromic hearing loss: a meta-analysis. JAMA Otolaryngology. 2023.
Medication Comparisons
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This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy