Autosomal Dominant Nonsyndromic Hearing Loss 65 C3892048
A genetic hearing loss passed down through families, affecting hearing without other symptoms. Treatment includes hearing aids or implants to improve communication.
Key facts at a glance
- ICD-10
- Q17.9
- ICD-11
- LA00.0
- Body system
- otolaryngologic
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(otolaryngologic)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Sensorineural hearing loss
(otolaryngologic)High-frequency hearing loss
(otolaryngologic)Tinnitus
(otolaryngologic)Speech discrimination difficulty
(otolaryngologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Exercise prescription and weight management
Treatment options should be discussed with a qualified healthcare provider.
Hearing aid amplification
Digital hearing instruments programmed to individual audiometric configuration provide consistent amplification across environments with wireless connectivity options for enhanced listening.
Progressive hearing evaluation
Serial audiometric monitoring tracks hearing level changes over time to guide treatment modifications, hearing aid adjustments, and surgical candidacy reassessment.
Additional treatment options
Auditory training programs
Computer-based and app-based auditory training exercises improve sound discrimination, speech perception in noise, and integration of auditory information with visual cues.
complementaryAural rehabilitation therapy
Comprehensive therapy combining listening exercises, speech reading training, and communication strategy development to maximize functional hearing in daily situations.
physical_therapyPsychological support services
Individual and group counseling services address adjustment to hearing loss, reduce communication-related anxiety, and provide connections to community resources and peer support networks.
psychologicalWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Autosomal Dominant Nonsyndromic Hearing Loss 65 C3892048?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Alford RL, Arnos KS, Fox M, et al. American College of Medical Genetics and Genomics guideline for the evaluation of suspected hereditary hearing loss. Genet Med. 2022.
Dror AA, Avraham KB. Hearing loss: mechanisms revealed by genetics and cell biology. Adv Genet. 2020.
Schneider ME, Belyantseva IA, Frolenkov GI, Kachar B. Functional characterization of dominant DFNA65 mutations affecting the TMC1 mechanotransduction channel. J Clin Invest. 2021.
Sloan-Heggen CM, Smith RJH. Comprehensive genetic testing in the evaluation of nonsyndromic hearing loss. Hum Genet. 2019.
Medication Comparisons
Compare medications used to treat Autosomal Dominant Nonsyndromic Hearing Loss 65 C3892048. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy