Autosomal Dominant Nonsyndromic Hearing Loss 66 C4283893
A hereditary form of hearing loss that runs in families, causing reduced hearing without affecting other organs. Sound amplification devices help manage the condition.
Key facts at a glance
- ICD-10
- Q17.9
- ICD-11
- LA00.0
- Body system
- otolaryngologic
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(otolaryngologic)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Sensorineural hearing loss
(otolaryngologic)Progressive hearing loss
(otolaryngologic)Bilateral hearing impairment
(otolaryngologic)Tinnitus
(otolaryngologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Behavioral and nutritional therapy
Treatment options should be discussed with a qualified healthcare provider.
Regular Audiological Monitoring
Scheduled hearing assessments every 6-12 months to track disease progression and adjust interventions as needed. Includes pure-tone audiometry, speech discrimination testing, and immittance testing.
Hearing Assistive Technology
Provision of personal amplifiers, TV listening devices, and alerting systems to improve daily functioning and communication access in various environments.
Additional treatment options
Hearing Aid Fitting
Custom-fitted amplification devices programmed to individual audiometric findings, with ongoing adjustment and counseling on proper use and maintenance.
procedureAudiologic Rehabilitation Counseling
Comprehensive counseling addressing communication strategies, lip-reading techniques, and psychosocial adjustment to living with progressive hearing loss.
psychologicalCochlear Implant Evaluation
Comprehensive candidacy assessment for cochlear implantation in patients with severe-to-profound hearing loss not adequately helped by conventional amplification.
surgicalWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Autosomal Dominant Nonsyndromic Hearing Loss 66 C4283893?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Shearer AE, Hildebrand MS, Sloan CM, Smith RJH. Deafness and Hereditary Hearing Loss Overview. GeneReviews. 2023.
Alford RL, Arnos KS, Fox M, et al. American College of Medical Genetics and Genomics guideline for the evaluation of nonsyndromic hearing loss and deafness. Genet Med. 2022.
Dror AA, Avraham KB. Hearing impairment: a new window into the pathogenesis of common forms of hearing loss. Trends Mol Med. 2021.
Yasuda M, Brownlee T, Kaga K. Molecular characterization of autosomal dominant nonsyndromic hearing loss in the Japanese population. Hum Genet. 2020.
Medication Comparisons
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This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy