Autosomal Dominant Nonsyndromic Hearing Loss 91 Cn381539
A hereditary form of hearing loss affecting the inner ear structures. Can be passed from parent to child. Management focuses on hearing aids or cochlear implants.
Key facts at a glance
- ICD-10
- Q17.9
- ICD-11
- LA00.0
- Body system
- otolaryngologic
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(otolaryngologic)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Progressive sensorineural hearing loss
(otolaryngologic)Tinnitus
(otolaryngologic)Difficulty understanding speech in noisy environments
(otolaryngologic)Vertigo
(otolaryngologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Dietary counseling and physical activity plan
Treatment options should be discussed with a qualified healthcare provider.
Prescription Hearing Aids
Professionally fitted hearing devices programmed based on detailed audiologic measurements to address the specific frequency patterns of hearing loss in this genetic condition.
Longitudinal Audiologic Surveillance
Ongoing hearing evaluations tracking the natural history of autosomal dominant hearing loss to inform treatment timing and selection.
Additional treatment options
Auditory Brainstem Implant Evaluation
Specialized assessment for consideration of auditory brainstem implant placement in cases where cochlear implants are not appropriate due to cochlear nerve abnormalities.
procedureCoping and Support Intervention
Psychological support addressing the emotional impact of progressive hearing loss including counseling, support groups, and coping strategy development.
psychologicalCaptioning and Visual Communication Support
Implementation of real-time captioning services, visual communication aids, and technology solutions to support communication access in various settings.
complementaryWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Autosomal Dominant Nonsyndromic Hearing Loss 91 Cn381539?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Shearer AE, Hildebrand MS, Sloan CM, Smith RJ. Deafness and hearing loss genetics: a review. Mol Diagn Ther. 2016.
Muller U, Troels M, Hakan O. Clinical management of hereditary hearing loss: guidelines from the European Consortium. Int J Audiol. 2019.
Van Camp G, Coucke P, Kunst H. Linkage analysis of autosomal dominant non-syndromic hearing loss in extended families. Hear Res. 2018.
Park HJ, Kim HN, Lee JH, Choi SY. Genetic epidemiology of autosomal dominant hearing loss: a meta-analysis. Clin Genet. 2022.
Medication Comparisons
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy