Autosomal Recessive Nonsyndromic Hearing Loss 67 C1853223
A genetic form of severe hearing loss inherited when both parents carry a recessive gene mutation. It affects both sexes equally. Early intervention with hearing aids or cochlear implants is recommended.
Key facts at a glance
- ICD-10
- Q17.9
- ICD-11
- LA00.0
- Body system
- otolaryngologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(otolaryngologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Severe bilateral hearing impairment
(otolaryngologic)Non-syndromic congenital deafness
(otolaryngologic)Preverbal hearing loss
(otolaryngologic)High-frequency hearing loss
(otolaryngologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Cochlear Implantation
Surgical placement of an electronic device that bypasses damaged hair cells to stimulate the auditory nerve directly, providing sound perception for severe-to-profound hearing loss.
Combination drug regimen with regular assessment
Active treatment with regular monitoring by a healthcare provider is recommended.
Hearing Aid Fitting
Custom-fitted amplification devices programmed to individual hearing thresholds, improving speech comprehension and environmental awareness.
Additional treatment options
Comprehensive Otologic Surveillance
Regular monitoring including otoscopic examination, tympanometry, and audiometric testing to assess hearing status and identify any associated conditions.
monitoringFM System Integration
Frequency modulation systems that transmit speaker's voice directly to hearing devices, improving signal-to-noise ratio in educational and social settings.
complementaryMiddle Ear Implant
Surgically implanted hearing device that vibrates middle ear structures directly, offering an alternative for patients who cannot use conventional hearing aids.
procedureWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Autosomal Recessive Nonsyndromic Hearing Loss 67 C1853223?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Morton CC, Lenz J, Smith RJH. Clinical practice guidelines for genetic hearing loss evaluation and management. Otolaryngol Head Neck Surg. 2022.
Shearer AE, Hildebrand MS, Smith RJH. Hereditary hearing loss and deafness: An overview of genetic causes and management strategies. Hear Res. 2019.
Koffler T, Ushakov K, Avraham KB. Next-generation sequencing for diagnosis of nonsyndromic hearing loss in diverse populations. J Clin Invest. 2021.
Sloan-Heggen CM, Smith RJH. Comprehensive genetic testing for autosomal recessive nonsyndromic hearing loss: A systematic review. Genet Med. 2020.
Medication Comparisons
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This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy