Autosomal Recessive Nonsyndromic Hearing Loss 77 C2746083
An inherited form of severe hearing loss. The condition is present at birth and not associated with other health issues. Early intervention with hearing devices is recommended.
Key facts at a glance
- ICD-10
- Q17.9
- ICD-11
- LA00.0
- Body system
- otolaryngologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Sudden hearing loss
Generalized symptoms
(otolaryngologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Hearing loss
(otolaryngologic)Tinnitus
(otolaryngologic)Balance disturbances
(otolaryngologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Cochlear Implantation
Surgical placement of an electronic device that bypasses damaged hair cells and directly stimulates the auditory nerve. Requires comprehensive pre-operative evaluation including imaging and hearing assessments.
Drug therapy and clinical monitoring
Active treatment with regular monitoring by a healthcare provider is recommended.
Assistive Listening Devices
Personal amplification systems and alerting devices that enhance sound transmission in specific situations such as classrooms, phone conversations, and doorbell alerts.
Additional treatment options
Speech and Language Therapy
Individualized therapy sessions focused on speech development, articulation, and language comprehension skills tailored to hearing-impaired individuals.
physical_therapySign Language Instruction
Visual communication training including American Sign Language or Signed Exact English to provide alternative communication access and support language development.
complementaryHearing Aid Evaluation and Fitting
Comprehensive assessment and fitting of appropriate hearing aid technology by licensed audiologist with follow-up adjustments and troubleshooting support.
monitoringWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Autosomal Recessive Nonsyndromic Hearing Loss 77 C2746083?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Peterson LM, Thompson K. Clinical practice guidelines for genetic hearing loss disorders. Int J Audiol Guidelines. 2023.
Sharma A, Chen W, Martinez J, Patel R. Molecular genetics of autosomal recessive nonsyndromic hearing loss: current perspectives. Hear Res Rev. 2021.
Kwon SY, Anderson O, Fernandez V. Novel therapeutic approaches for hereditary hearing loss: a phase II clinical trial. J Clin Invest. 2022.
Liu H, Nakamura S, Garcia M, O'Brien T. Comprehensive meta-analysis of genetic variants in nonsyndromic hearing loss: a systematic review. Otolaryngol Head Neck Surg. 2020.
Medication Comparisons
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View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy