Autosomal Recessive Nonsyndromic Hearing Loss 83 C3888310
A hereditary cause of severe hearing loss without other symptoms. It follows autosomal recessive inheritance. Hearing aids, implants, and early speech intervention are used.
Key facts at a glance
- ICD-10
- Q17.9
- ICD-11
- LA00.0
- Body system
- otolaryngologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Sudden hearing loss
Generalized symptoms
(otolaryngologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Hearing loss
(otolaryngologic)Tinnitus
(otolaryngologic)Balance disturbances
(otolaryngologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Cochlear Implantation
Surgical placement of an electronic device that directly stimulates the auditory nerve, bypassing damaged hair cells in the cochlea to restore hearing perception.
Combination drug regimen with regular assessment
Active treatment with regular monitoring by a healthcare provider is recommended.
Digital Hearing Aids
Prescription-grade amplification devices programmed to the individual's specific audiometric profile to enhance sound perception and speech comprehension.
Additional treatment options
Comprehensive Audiological Surveillance
Regular hearing assessments including audiometry, tympanometry, and evoked potential testing to monitor disease progression and treatment efficacy.
monitoringAuditory-Verbal Therapy
Specialized therapy focusing on developing listening skills and spoken language through structured auditory training exercises and parent-guided home practice.
physical_therapyAssistive Listening Devices and Environmental Modifications
Personal and classroom amplification systems, alerting devices, and environmental adaptations to improve communication access in daily life.
lifestyleWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Autosomal Recessive Nonsyndromic Hearing Loss 83 C3888310?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Shearer AE, Hildebrand MS, Sloan CM, Smith RJ. Deafness and Hereditary Hearing Loss Overview. GeneReviews. 2011.
American College of Medical Genetics and Genomics. Genetics Evaluation Guidelines for Etiologic Diagnosis of Congenital Hearing Loss. Genet Med. 2012.
Brownstein Z, Bhatt S, Dror AA, Sagi-Dain L, Avraham KB. Targeted Gene Panel Sequencing for Autosomal Recessive Non-Syndromic Hearing Loss. Mol Diagn Ther. 2019.
Sloan-Heggen CM, Babanejad M, Beheshtian M, et al. Molecular Epidemiology of Nonsyndromic Hearing Loss in 125 Patients. JAMA Otolaryngol Head Neck Surg. 2016.
Medication Comparisons
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View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 25, 2026. · Read our editorial policy