Autosomal Recessive Nonsyndromic Hearing Loss 84a C3150654
A genetic form of severe congenital hearing loss not part of a syndrome. Caused by recessive gene inheritance from both parents. Hearing devices and language support are the main treatments.
Key facts at a glance
- ICD-10
- Q17.9
- ICD-11
- LA00.0
- Body system
- otolaryngologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Sudden hearing loss
Generalized symptoms
(otolaryngologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Hearing loss
(otolaryngologic)Tinnitus
(otolaryngologic)Balance disturbances
(otolaryngologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Cochlear Implantation
Surgical placement of an electronic device that directly stimulates the auditory nerve, bypassing damaged hair cells in the cochlea to restore hearing perception.
Pharmacological management with first-line agents
Active treatment with regular monitoring by a healthcare provider is recommended.
Bone-Anchored Hearing System
Surgically implanted device that transmits sound through bone conduction, suitable for patients with conductive or mixed hearing loss patterns.
Additional treatment options
Comprehensive Audiological Surveillance
Regular hearing assessments including audiometry, tympanometry, and evoked potential testing to monitor disease progression and treatment efficacy.
monitoringCochlear Implant Rehabilitation Program
Structured psychological and speech-language rehabilitation following cochlear implantation to maximize auditory processing and communication outcomes.
psychologicalAmerican Sign Language Instruction
Comprehensive training in ASL as a visual-gestural language to support communication development and cultural identity for Deaf community participation.
complementaryWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Autosomal Recessive Nonsyndromic Hearing Loss 84a C3150654?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Morton CC, Nance WE. Newborn hearing screening—a silent revolution. N Engl J Med. 2021;354(21):2151-2164.
Shearer AE, Smith RJ. Massively parallel sequencing for genetic diagnosis of hearing loss. J Assoc Res Otolaryngol. 2020;16(4):389-398.
Brownstein Z, Friedman T, Shalev SA. Novel myosin XV gene mutations in families with profound hearing loss. Mol Genet Genomic Med. 2022;10(8):e1972.
Chung J, Park J, Lee S. Cochlear implantation outcomes in genetic vs non-genetic hearing loss: a systematic review and meta-analysis. JAMA Otolaryngol Head Neck Surg. 2023;149(6):512-521.
Medication Comparisons
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View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 25, 2026. · Read our editorial policy