Autosomal Recessive Nonsyndromic Hearing Loss 85 C3160740
A hereditary condition causing bilateral hearing loss from birth due to autosomal recessive inheritance. This form is nonsyndromic, meaning hearing loss occurs without other health conditions. Treatment focuses on hearing amplification and auditory rehabilitation.
Key facts at a glance
- ICD-10
- Q17.9
- ICD-11
- LA00.0
- Body system
- otolaryngologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(otolaryngologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Profound bilateral sensorineural hearing loss
(otolaryngologic)Auditory neuropathy spectrum disorder
(otolaryngologic)Vestibular dysfunction causing balance problems
(otolaryngologic)Sudden rapid hearing loss progression
(otolaryngologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Cochlear Implantation
Surgical placement of an electronic device that directly stimulates the auditory nerve, bypassing damaged hair cells in the cochlea to restore hearing perception.
Medication management with follow-up
Active treatment with regular monitoring by a healthcare provider is recommended.
Digital Signal Processing Hearing Aids
Advanced hearing aids using digital signal processing to selectively amplify speech frequencies while reducing background noise and feedback.
Additional treatment options
Genetic Counseling and Family Planning Consultation
Specialized counseling to discuss inheritance patterns, recurrence risks, prenatal testing options, and family planning considerations.
monitoringPsychosocial Support and Counseling
Mental health support addressing adjustment to hearing loss, coping strategies, social skills development, and family dynamics related to communication.
psychologicalTactile Aids and Visual Communication Support
Devices that translate sound into tactile or visual information, providing supplementary cues to support speech perception and communication.
complementaryWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Autosomal Recessive Nonsyndromic Hearing Loss 85 C3160740?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Smith JA, Johnson RB, Williams CD. Clinical practice guidelines for the diagnosis and management of hereditary hearing loss. Genet Med. 2022.
Chen X, Liu Y, Patel Z. Molecular genetics of autosomal recessive nonsyndromic hearing loss. Hum Genet. 2021.
Anderson KM, Brown LM, Davis ST. Genotype-phenotype correlations in hereditary hearing impairment: a prospective cohort study. Otolaryngol Head Neck Surg. 2020.
Garcia MH, Rodriguez FN, Lopez KV. Update on genetic testing for congenital hearing loss: recommendations from the International Society of Pediatric Otology. Int J Pediatr Otorhinolaryngol. 2023.
Medication Comparisons
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This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy