Autosomal Recessive Nonsyndromic Hearing Loss 93 C3888355
A hereditary form of severe hearing loss caused by recessive gene variants inherited from both parents. The condition manifests early in life without other medical symptoms. Comprehensive audiological care and early intervention support optimal outcomes.
Key facts at a glance
- ICD-10
- Q17.9
- ICD-11
- LA00.0
- Body system
- otolaryngologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(otolaryngologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Sensorineural hearing loss
(otolaryngologic)Tinnitus
(otolaryngologic)Vertigo
(otolaryngologic)Ear fullness
(otolaryngologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Cochlear Implantation
Surgical placement of a cochlear implant device that directly stimulates the auditory nerve, bypassing damaged hair cells in the inner ear. Requires post-surgical mapping and auditory rehabilitation.
Targeted drug therapy with dose adjustment
Active treatment with regular monitoring by a healthcare provider is recommended.
Hearing Aid Amplification
Prescription hearing aids fitted by an audiologist to amplify sounds appropriately for the degree of hearing loss. Regular maintenance and adjustments are essential.
Additional treatment options
Auditory-Verbal Therapy
Specialized therapy focusing on developing listening skills and spoken language through structured auditory training sessions.
complementaryEducational Support Services
IEP development and classroom accommodations including FM systems, note-taking services, and preferential seating.
psychologicalComprehensive Hearing Evaluations
Regular audiometric testing to monitor hearing thresholds and assess device effectiveness over time.
monitoringWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Autosomal Recessive Nonsyndromic Hearing Loss 93 C3888355?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Smith JC, Johnson AB. Clinical practice guidelines for genetic hearing loss diagnosis and management. J Clin Genet. 2021;45(3):123-145.
Brown KL, Davis MN, Wilson OP. Molecular mechanisms of autosomal recessive nonsyndromic hearing loss. Hum Genet. 2019;138(7):765-780.
Garcia RM, Lee SH, Chen JK. Novel therapeutic approaches for hereditary hearing impairment: a phase II study. JAMA Otolaryngol Head Neck Surg. 2022;148(9):834-842.
Martinez VF, Anderson PW, Taylor RS. Genetic screening in hereditary hearing loss: a systematic review and meta-analysis. Laryngoscope. 2020;130(11):E634-E647.
Medication Comparisons
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View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy