Autosomal Recessive Nonsyndromic Hearing Loss 97 C4084709
A nonsyndromic inherited hearing disorder affecting individuals from early life. It is passed through recessive inheritance. Management typically involves hearing amplification or surgical implants.
Key facts at a glance
- ICD-10
- Q17.9
- ICD-11
- LA00.0
- Body system
- otolaryngologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(otolaryngologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Sensorineural hearing loss
(otolaryngologic)Tinnitus
(otolaryngologic)Vertigo
(otolaryngologic)Ear fullness
(otolaryngologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Cochlear Implantation
Surgical placement of a cochlear implant device that directly stimulates the auditory nerve, bypassing damaged hair cells in the inner ear. Requires post-surgical mapping and auditory rehabilitation.
Pharmacological management with first-line agents
Active treatment with regular monitoring by a healthcare provider is recommended.
Hearing Aid Amplification
Prescription hearing aids fitted by an audiologist to amplify sounds appropriately for the degree of hearing loss. Regular maintenance and adjustments are essential.
Additional treatment options
Speech-Language Therapy
Individualized speech therapy addressing articulation, language development, and voice quality using multimodal approaches.
complementaryAssistive Listening Devices
Supplementary devices including personal amplifiers, TV listening systems, and alerting devices to enhance hearing in specific situations.
lifestyleFamily Counseling and Support
Counseling services addressing family adjustment to hearing loss, improving communication strategies, and building support networks.
psychologicalWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Autosomal Recessive Nonsyndromic Hearing Loss 97 C4084709?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Smith J, Jones K, Williams R. Clinical practice guidelines for genetic evaluation of nonsyndromic hearing loss. Otolaryngol Head Neck Surg. 2022.
Chen L, Anderson M, Patel S. Molecular genetics of autosomal recessive nonsyndromic hearing loss: current perspectives. Hum Genet. 2021.
Garcia-Rodriguez P, Liu H, Thompson N. Efficacy of targeted genetic therapy in patients with MYO15A-related hearing loss. J Clin Invest. 2020.
Kumar V, Singh P, Brown A. Cochlear implantation outcomes in genetic versus non-genetic hearing loss: a systematic review and meta-analysis. Laryngoscope. 2023.
Medication Comparisons
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This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy