Bicuspid Aortic Valve With Left Noncoronary Cusp Fusion C4476981
This is a variant of bicuspid aortic valve where the left and noncoronary cusps are fused together. It is a congenital condition that may be discovered in adulthood. Regular cardiac monitoring helps track valve function over time.
Key facts at a glance
- ICD-10
- Q23.81
- ICD-11
- LA00.0
- Body system
- cardiovascular
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Syncope
Cardiac murmur
(cardiovascular)Chest discomfort or palpitations
(cardiovascular)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Fatigue with exertion
(cardiovascular)Pedal edema
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Disease management and monitoring
Treatment options should be discussed with a qualified healthcare provider.
Intensive cardiac imaging surveillance
Regular cardiac MRI and echocardiography to monitor the specific fusion pattern, valve function, and ascending aorta dimensions given the unique hemodynamics of left noncoronary cusp fusion.
Valve-sparing aortic root replacement
Specialized surgical approach preserving the native valve while replacing the dilated ascending aorta, potentially advantageous for younger patients with this fusion pattern.
Additional treatment options
Aortic valve repair with cusp fusion modification
Surgical repair technique specific to bicuspid valves with left noncoronary fusion, attempting to restore more physiological valve function.
surgicalBeta-blocker therapy for aortic stress reduction
Pharmacologic reduction of aortic wall stress through heart rate and blood pressure control, particularly when aortic dilation approaches intervention thresholds.
medicationHemodynamic optimization
Lifestyle modifications including blood pressure control, smoking cessation, and avoidance of strenuous isometric exercise to minimize aortic stress.
lifestyleWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Bicuspid Aortic Valve With Left Noncoronary Cusp Fusion C4476981?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
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This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy