Bicuspid Aortic Valve With Right Left Cusp Fusion C4476979
This bicuspid aortic valve variant involves fusion of the right and left coronary cusps. Like other forms, it is a congenital heart defect present from birth. Ongoing cardiac evaluation is recommended to monitor for complications.
Key facts at a glance
- ICD-10
- Q23.81
- ICD-11
- LA00.0
- Body system
- cardiovascular
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Chest discomfort or palpitations
(cardiovascular)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Heart murmur
(cardiovascular)Dyspnea on exertion
(cardiovascular)Fatigue
(cardiovascular)Palpitations
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Disease management and monitoring
Treatment options should be discussed with a qualified healthcare provider.
Regular Cardiac Monitoring
Periodic echocardiograms and clinical evaluations to track aortic valve function, aortic root dimensions, and detect any progression of stenosis or regurgitation.
Symptom Management Medications
Beta-blockers or other cardiac medications may be prescribed to manage blood pressure, reduce cardiac workload, and control symptoms of heart failure if they develop.
Additional treatment options
Aortic Valve Repair or Replacement
Surgical intervention to repair or replace the defective valve, recommended when significant stenosis or regurgitation develops or aortic root dilation occurs.
surgicalActivity Modification
Avoidance of competitive sports and heavy weightlifting that significantly increase aortic stress. Low-to-moderate aerobic exercise typically permitted.
lifestyleTranscatheter Aortic Valve Implantation (TAVI)
Minimally invasive procedure to implant a new valve via catheter for patients at high surgical risk, increasingly used for suitable candidates.
procedureWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Bicuspid Aortic Valve With Right Left Cusp Fusion C4476979?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
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This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy