Bilateral Multicystic Dysplastic Kidney C1840451
A congenital condition where both kidneys develop abnormally with multiple cysts instead of functioning tissue. This causes kidney failure in newborns and requires dialysis or kidney transplant for survival.
Key facts at a glance
- ICD-10
- N28.9
- ICD-11
- GA00.0
- Body system
- renal
- Severity
- critical
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Changes in urination or swelling
Symptoms may be severe and require urgent medical attention.
Seek immediate emergency care if symptoms are severe or worsening rapidly.
Oliguria
Neonatal renal failure
(renal)Hypertension
(renal)Urinary tract infection
(renal)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Renal disease management
Requires immediate emergency medical intervention. Do not delay treatment.
Renal Function Surveillance
Close monitoring of remaining renal function through regular creatinine, electrolytes, and imaging studies to assess kidney disease progression.
Renal Replacement Therapy Planning
Preparation for and initiation of dialysis or kidney transplantation as definitive treatment for end-stage renal disease from bilateral kidney dysfunction.
Additional treatment options
Nephrology Specialist Management
Long-term management by pediatric or adult nephrology team including blood pressure control, electrolyte management, and growth monitoring.
monitoringFamily Education and Support
Comprehensive education for caregivers on renal diet modifications, medication administration, recognizing signs of complications, and managing dialysis requirements.
lifestyleKidney Transplant Evaluation
Comprehensive pre-transplant assessment including tissue typing, sensitization evaluation, and identification of suitable donors for definitive renal replacement.
surgicalWhen to seek medical help
Recognize when you need immediate medical attention.
Call emergency services (911) immediately
Signs of serious or life-threatening complications associated with this condition. Immediate medical evaluation is required.
Seek emergency medical care immediately if experiencing: difficulty breathing, chest pain, sudden severe headache, loss of consciousness, sudden weakness or numbness, or signs of internal bleeding.
Frequently asked questions
Common questions about this topic.
What is Bilateral Multicystic Dysplastic Kidney C1840451?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Nguyen HT, Benson CB, Bromley B, et al. Multicystic dysplastic kidney and renal agenesis: definition and management. J Urol. 2022;208(3):558-567.
Kumar S, Chandna SM, Ratan SK. Bilateral multicystic dysplastic kidney: a rare entity with management challenges. Pediatr Nephrol. 2021;36(12):3791-3802.
Rasouly HM, Lu W, Lakhia R, et al. Lower urinary tract development and renal cystic phenotypes in congenital abnormalities. Kidney Int. 2020;97(5):950-964.
Schoenbuhn SM, Schreider J, Gimpel C. Long-term outcomes in multicystic dysplastic kidney disease: systematic review. Nephrol Dial Transplant. 2023;38(6):1458-1468.
Medication Comparisons
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View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy