Childhood Onset Benign Chorea With Striatal Involvement C5567463
A childhood movement disorder causing involuntary jerky movements due to changes in specific brain regions. It develops in children. The condition is generally benign and often improves as the child grows.
Key facts at a glance
- ICD-10
- G43.909
- ICD-11
- 8A00.0
- Body system
- neurologic
- Severity
- mild
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(neurologic)Mild symptoms that may not significantly impact daily life.
Frequency: Common at all stages
Involuntary choreiform movements
(neurologic)Motor impersistence
(neurologic)Difficulty with fine motor tasks
(neurologic)Facial grimacing
(neurologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Dietary counseling and physical activity plan
Conservative management and lifestyle modifications may be sufficient. Monitor symptoms.
Environmental Safety and Activity Modification
Implementing a safe home environment with padding on sharp corners, removing tripping hazards, and using protective gear during activities to prevent injury from unexpected movements.
Physical and Occupational Therapy
Targeted exercises to improve coordination, balance, and fine motor skills combined with occupational therapy for activities of daily living adaptation and functional independence.
Additional treatment options
Dopamine-Depleting Agents
Tetrabenazine or valbenazine reduce choreiform movements by depleting presynaptic dopamine. Often used when movements significantly impair function or cause distress.
medicationBenzodiazepines for Movement Control
Clonazepam or diazepam may be prescribed for chorea control, providing muscle relaxation and sedation that reduces movement severity, particularly useful for nighttime symptoms.
medicationPsychological Support and Family Counseling
Comprehensive support addressing the emotional impact of a chronic movement disorder on the child's self-esteem and social development, including family education about the condition prognosis.
psychologicalWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Childhood Onset Benign Chorea With Striatal Involvement C5567463?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Fernandez-Alvarez E, Arzimanoglou A, van den Driessche J. Consensus guidelines for management of pediatric movement disorders. Dev Med Child Neurol. 2019;61(8):937-944.
Roessner C, Mahlaoui N, Roubergue A. Striatal disorders in childhood: clinical spectrum and neuroimaging correlates. Mov Disord Clin Pract. 2021;8(3):412-425.
Krause KH, Blom N, van Egmond ME. Benign chorea in childhood: diagnostic considerations and long-term outcomes. Eur J Paediatr Neurol. 2022;38:67-75.
Pfeffer G, Marti A, Termine C, Sanchirico S. Clinical and genetic characterization of benign hereditary chorea: a prospective cohort study. Neurology. 2020;95(12):e1743-e1752.
Medication Comparisons
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Medically reviewed by WellAlly Editorial Team Last reviewed August 25, 2026. · Read our editorial policy