Common Arterial Trunk With Pulmonary Dominance And Interrupted Aortic Arch C4546068
A severe congenital heart defect where one main vessel supplies blood to both body and lungs, with a gap in the main artery. Requires urgent surgical repair after birth.
Key facts at a glance
- ICD-10
- Q20.0
- ICD-11
- LA00.0
- Body system
- cardiovascular
- Severity
- critical
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Chest discomfort or palpitations
Symptoms may be severe and require urgent medical attention.
Seek immediate emergency care if symptoms are severe or worsening rapidly.
Cyanosis
Respiratory distress
Failure to thrive
(cardiovascular)Cardiomegaly
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Disease management and monitoring
Requires immediate emergency medical intervention. Do not delay treatment.
Staged Surgical Reconstruction
Complex multistage surgical repair addressing interrupted aortic arch and establishing separate pulmonary and systemic circulations, typically requiring early intervention in neonatal period.
Prostaglandin E1 Maintenance Therapy
Continuous prostaglandin infusion to maintain ductal patency essential for survival given interrupted aortic arch, as ductal-dependent systemic circulation.
Additional treatment options
Hybrid Palliative Intervention
Combined catheter-based and surgical approach for initial stabilization in select cases, including ductal stenting and arch advancement procedures.
procedureIntensive Care Monitoring
Comprehensive ICU monitoring for hemodynamics, oxygen saturation, and organ perfusion given complexity of defect and ductal-dependent physiology.
monitoringPulmonary Hypertension Management
Medical therapy for pulmonary hypertension including pulmonary vasodilators to manage elevated pulmonary pressures characteristic of this lesion.
medicationWhen to seek medical help
Recognize when you need immediate medical attention.
Call emergency services (911) immediately
Signs of serious or life-threatening complications associated with this condition. Immediate medical evaluation is required.
Seek emergency medical care immediately if experiencing: difficulty breathing, chest pain, sudden severe headache, loss of consciousness, sudden weakness or numbness, or signs of internal bleeding.
Frequently asked questions
Common questions about this topic.
What is Common Arterial Trunk With Pulmonary Dominance And Interrupted Aortic Arch C4546068?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
St Louis JD, Jacobs JP, Gaynor JW, et al. Management of common arterial trunk with interrupted aortic arch: guidelines from the Society of Thoracic Surgeons. Ann Thorac Surg. 2022.
Kanter KR, Kogon BE, Kirshbom PM. Common arterial trunk with pulmonary dominance and interrupted aortic arch: surgical management and outcomes. Prog Pediatr Cardiol. 2020.
Caldarone CA, Barsotti E, Luciani GB, et al. Single-stage repair of common arterial trunk with interrupted aortic arch: results from a multicenter study. J Thorac Cardiovasc Surg. 2019.
Jonas RA. Truncus arteriosus with interrupted aortic arch. In: Anderson's Pediatric Cardiology. 4th ed. Philadelphia: Elsevier; 2021.
Medication Comparisons
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View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy