Congenital Stationary Night Blindness 1a C3495587
An inherited eye disorder that causes difficulty seeing in low light or darkness. This condition is present from birth and does not worsen over time. Management focuses on adapting the environment and using visual aids.
Key facts at a glance
- ICD-10
- Q15.9
- ICD-11
- LA00.0
- Body system
- ophthalmologic
- Severity
- mild
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(ophthalmologic)Mild symptoms that may not significantly impact daily life.
Frequency: Common at all stages
Night blindness
(ophthalmologic)Reduced visual acuity in low light
(ophthalmologic)Myopia
(ophthalmologic)Visual field constriction
(ophthalmologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Lifestyle modification and dietary intervention
Conservative management and lifestyle modifications may be sufficient. Monitor symptoms.
Environmental Adaptation and Safety
Modification of living and working environments to enhance safety in low-light conditions. Includes proper lighting, contrast enhancement, and removal of hazards that are difficult to see at night.
Low Vision Aid Consultation
Assessment and provision of assistive devices such as tinted lenses, magnifying devices, and specialized lighting to maximize remaining vision. Training in effective use of these aids for daily activities.
Additional treatment options
Regular Ophthalmologic Evaluation
Periodic eye examinations to monitor for associated ocular conditions, assess visual function, and update corrective prescriptions. Includes evaluation for nystagmus or strabismus that may accompany the condition.
monitoringVision Rehabilitation Counseling
Support services addressing the psychosocial impact of lifelong visual impairment, including strategies for independence, driving limitations discussion, and career planning considerations.
psychologicalOccupational Therapy for Daily Living
Training in techniques and use of adaptive equipment for independent functioning despite night blindness. Includes cooking, personal care, and mobility strategies optimized for low-light conditions.
lifestyleWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Congenital Stationary Night Blindness 1a C3495587?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Berger RW, Neuhaus C, Dollfus H. Molecular genetics of congenital stationary night blindness. Orphanet J Rare Dis. 2022.
Kellner U, Zobor D, Bach M, et al. Consensus guidelines for diagnostics and therapy of congenital stationary night blindness. Clin Exp Ophthalmol. 2021.
Tsang SH, Sharma T, Hussain K, et al. Clinical characterization and natural history of CSNB1A: ERG and molecular findings. Invest Ophthalmol Vis Sci. 2020.
Michaelides M, Hunt DM, Moore AT. The genetics of inherited retinal dystrophies. In: Ryan SJ, ed. Retina. 6th ed. Elsevier; 2023.
Medication Comparisons
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy