Deafness X Linked 5 C1845095
A genetic form of hearing loss passed through the X chromosome, primarily affecting males. People are typically born with or develop hearing loss in early childhood. Amplification devices and communication therapies are the main treatments.
Key facts at a glance
- ICD-10
- Q17.9
- ICD-11
- LA00.0
- Body system
- otolaryngologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Congenital severe sensorineural hearing loss
(otolaryngologic)Generalized symptoms
(otolaryngologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Progressive hearing loss in adolescence
(otolaryngologic)Tinnitus
(otolaryngologic)Episodic vertigo
(otolaryngologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Cochlear Implantation
Surgical insertion of an electrode array into the cochlea to provide direct electrical stimulation of the auditory nerve, bypassing the damaged structures characteristic of X-linked deafness.
Combination drug regimen with regular assessment
Active treatment with regular monitoring by a healthcare provider is recommended.
Bone-Anchored Hearing System
Surgically implanted hearing device that transmits sound through bone conduction, particularly useful when middle ear abnormalities preclude conventional hearing aids.
Additional treatment options
Communication Skills Development
Comprehensive speech-language therapy and aural rehabilitation services tailored to individual hearing levels and communication preferences, including lip-reading instruction.
psychologicalRegular Audiologic Surveillance
Scheduled hearing evaluations and medical follow-up to monitor disease progression and device function, with adjustments to treatment plans as needed.
monitoringSign Language and Visual Communication Training
Acquisition of sign language skills as an alternative or supplementary communication method to support overall communication access and cultural identity.
complementaryWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Deafness X Linked 5 C1845095?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalMedication Comparisons
Compare medications used to treat Deafness X Linked 5 C1845095. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy