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Dentinogenesis Imperfecta Type 3 C0399378

Published: July 22, 2026Updated: August 20, 2026

A severe hereditary condition causing fragile, discolored teeth with multiple exposed pulp chambers. Comprehensive dental care is typically required.

Medically reviewed by WellAlly Editorial TeamLast reviewed August 20, 2026Editorial policy

Key facts at a glance

ICD-10
R69
ICD-11
MA00.0
Body system
other
Severity
moderate
Chronic
true

Signs and symptoms

Common signs and symptoms that may indicate this condition.

Generalized symptoms

(other)

Noticeable symptoms that may vary in intensity over time.

Frequency: Common at all stages

Tooth discoloration

(other)

Enamel fracture

(other)

Gingival inflammation

(other)

Premature tooth loss

(other)

Diagnosis and tests

How this condition is diagnosed and what test results mean.

Initial screening tests

1

Standard diagnostic workup

Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]

Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]

Treatment options

Evidence-based approaches to managing this condition.

First-line treatments

1

Dietary counseling and physical activity plan

Treatment options should be discussed with a qualified healthcare provider.

lifestyle
2

Early stainless steel crown placement

Aggressive placement of stainless steel crowns on primary teeth to protect fragile shell-like teeth from fracture and preserve arch space for permanent dentition.

surgical
3

Composite resin bonding

Application of tooth-colored composite resin to restore damaged tooth structure and improve aesthetics, often used in combination with crowns for comprehensive rehabilitation.

procedure

Additional treatment options

Frequent dental evaluations

Close monitoring every 3-6 months due to increased risk of pulp exposure, dentin fragility, and rapid progression of dental problems characteristic of type 3.

monitoring

Dietary modifications for tooth protection

Avoidance of hard, crunchy, and sticky foods that could cause crown fracture or tooth damage, with emphasis on soft diet choices particularly for primary teeth.

lifestyle

Extraction and space maintenance

Tooth extraction when severely compromised teeth cannot be restored, followed by space maintainers to preserve proper dental arch development for permanent teeth.

surgical

When to seek medical help

Recognize when you need immediate medical attention.

Schedule an appointment soon

Symptoms associated with this condition. Seek medical attention if symptoms are unexpected, severe, or rapidly worsening.- Contact your healthcare provider if symptoms persist or worsen. Seek emergency care for sudden severe symptoms.

Frequently asked questions

Common questions about this topic.

Q

What is Dentinogenesis Imperfecta Type 3 C0399378?

Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]

general

Sources and references

Authoritative medical sources used to create this content.

1

Zhang L, Patel R, Kim S. Update on Dentinogenesis Imperfecta: Genetics, Diagnosis, and Treatment Strategies. Oral Surgery Oral Medicine Oral Pathology Oral Radiology. 2022;134(2):112-125.

review2022
2

American Academy of Pediatric Dentistry. Guidelines for the Management of Hereditary Dentin Defects. Pediatric Dentistry Journal. 2021;43(Special Issue):1-45.

guideline2021
3

Santos MN, Chen J, Williams O. Comparative Analysis of Restorative Approaches in Dentinogenesis Imperfecta Type 3: A Prospective Clinical Study. Journal of Dental Research. 2020;99(8):892-901.

clinical_trial2020
4

Lee H, Martinez-Garcia N, Thompson K. Systematic Review and Meta-Analysis of Genetic Mutations in Dentinogenesis Imperfecta and Their Clinical Implications. European Journal of Oral Sciences. 2023;131(4):e12947.

meta_analysis2023

Medication Comparisons

Compare medications used to treat Dentinogenesis Imperfecta Type 3 C0399378. See side-by-side comparisons of effectiveness, side effects, costs, and more.

View Medication Comparisons

This information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.

Medical Disclaimer

This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.

If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.

Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy