Developmental And Epileptic Encephalopathy 65 C4693925
A complex neurological disorder with early seizures and developmental challenges in children. Treatment focuses on seizure management and maximizing quality of life.
Key facts at a glance
- ICD-10
- G40.909
- ICD-11
- 8A00.0
- Body system
- neurologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Epileptic spasms in clusters
Generalized symptoms
(neurologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Profound developmental regression
(neurologic)Generalized dystonia
(neurologic)Cortical visual impairment
(neurologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Drug therapy and clinical monitoring
Active treatment with regular monitoring by a healthcare provider is recommended.
Targeted anti-seizure pharmacotherapy
Individualized medication regimen based on specific seizure semiology and genetic background when available. Multiple ASMs may be needed to achieve seizure control.
Modified Atkins diet
Less restrictive alternative to ketogenic diet, offering similar seizure reduction benefits with more flexibility. May be better tolerated long-term.
Additional treatment options
Cognitive behavioral and family support therapy
Psychological interventions addressing behavioral challenges, anxiety, and family coping strategies. Essential for managing the emotional impact of severe epilepsy.
psychologicalMusic therapy and auditory stimulation
Non-invasive approach using structured music exposure to potentially reduce seizure activity and improve cognitive engagement. Evidence varies by individual response.
complementaryResective epilepsy surgery evaluation
Comprehensive pre-surgical assessment including video-EEG monitoring, MRI, and PET scanning to identify potentially resectable seizure foci.
surgicalWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Developmental And Epileptic Encephalopathy 65 C4693925?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
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This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 26, 2026. · Read our editorial policy