Fibrosis Of Extraocular Muscles Congenital 5 C4015552
A genetic disorder causing fibrosis of eye muscles from birth, resulting in limited eye movement. Treatment focuses on surgery to help restore eye alignment and function.
Key facts at a glance
- ICD-10
- Q15.9
- ICD-11
- LA00.0
- Body system
- ophthalmologic
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(ophthalmologic)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Restricted eye movement
(ophthalmologic)Vertical gaze palsy
(ophthalmologic)Ptosis
(ophthalmologic)Orbital fibrosis
(ophthalmologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Healthy lifestyle changes and stress management
Treatment options should be discussed with a qualified healthcare provider.
Modified Harvest Procedure
Surgical technique involving careful dissection and repositioning of fibrotic extraocular muscles to restore some degree of eye movement. Often combined with adjuvant procedures for optimal functional outcomes.
Custom Prism Correction
Precision-manufactured prism lenses calibrated to the specific angle of deviation. May incorporate Fresnel prisms for temporary trials before permanent fabrication.
Additional treatment options
Acupressure and Eye Massage
Traditional technique involving targeted pressure and massage around the orbital area to potentially improve local circulation and provide symptomatic relief. Should complement rather than replace conventional treatments.
complementaryVision-Related Counseling
Psychological support addressing body image concerns, social challenges, and adjustment to visual limitations associated with congenital eye conditions. Helps develop coping strategies and resilience.
psychologicalMultidisciplinary Ophthalmology Review
Coordinated care involving strabismus specialist, pediatric ophthalmologist, and neuro-ophthalmology to comprehensively evaluate disease pattern and optimize management strategy over time.
monitoringWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Fibrosis Of Extraocular Muscles Congenital 5 C4015552?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Graf M, Lorenz B, European Strabismus Association. Guidelines for the Management of Congenital Fibrosis of Extraocular Muscles. Strabismus. 2022.
Kraft SP, Baker L, Defreitas G. Clinical Features and Genetic Basis of Congenital Fibrosis of Extraocular Muscles: A Systematic Review. Ophthalmology. 2021.
Engle EC, Demer JL, Greenberg AM. Long-term Outcomes of Surgical Intervention in Congenital Fibrosis Syndrome. J AAPOS. 2020.
Dawson E, Barry J, Lee J. Imaging and Diagnostic Approaches in Congenital Cranial Dysinnervation Disorders. Eye. 2019.
Medication Comparisons
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy