Glaucoma 3 Primary Congenital E C4310639
A genetic form of congenital glaucoma affecting eyes from birth. It involves improper eye drainage leading to high pressure. Prompt surgical treatment is essential for vision preservation.
Key facts at a glance
- ICD-10
- Q15.9
- ICD-11
- LA00.0
- Body system
- ophthalmologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Buphthalmos
Generalized symptoms
(ophthalmologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Blepharospasm
(ophthalmologic)Excessive tearing
(ophthalmologic)Headache associated with ocular pain
(ophthalmologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Medication management with follow-up
Active treatment with regular monitoring by a healthcare provider is recommended.
Primary Goniotomy
First-line surgical intervention for this form of congenital glaucoma when corneal transparency permits visualization of the angle structures. Creates controlled opening in the trabecular meshwork.
Additional treatment options
Baerveldt Implant Surgery
Non-valved glaucoma drainage device implantation for long-term intraocular pressure control. Shunts aqueous humor to a subconjunctival reservoir.
surgicalSystemic Carbonic Anhydrase Inhibitors
Oral acetazolamide used short-term in acute settings to rapidly reduce intraocular pressure when topical therapy insufficient. Addresses both production and outflow mechanisms.
medicationMydriatic-Cycloplegic Agents
Agents like atropine used to prevent synechiae formation and stabilize the pupil after surgery. May also reduce discomfort from ciliary spasm.
medicationGeneral Anesthesia for Comprehensive Examination
Examination under anesthesia allows accurate measurement of intraocular pressure, corneal diameter, axial length, and direct visualization of angle structures when examination awake is unreliable.
procedureWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Glaucoma 3 Primary Congenital E C4310639?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalMedication Comparisons
Compare medications used to treat Glaucoma 3 Primary Congenital E C4310639. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy