Hearing Loss Autosomal Dominant 71 C4539881
An inherited form of hearing loss passed down in families through autosomal dominant inheritance. Treated with hearing aids or cochlear implants.
Key facts at a glance
- ICD-10
- Q17.9
- ICD-11
- LA00.0
- Body system
- otolaryngologic
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(otolaryngologic)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Post-lingual progressive hearing loss
(otolaryngologic)High-frequency sensorineural hearing loss
(otolaryngologic)Non-pulsatile tinnitus
(otolaryngologic)Vestibular balance disturbances
(otolaryngologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Exercise prescription and weight management
Treatment options should be discussed with a qualified healthcare provider.
Hearing Aid Amplification
Prescription hearing aids calibrated to individual audiometric findings amplify environmental sounds and speech frequencies affected by genetic hearing loss. Modern digital hearing aids offer adaptive noise reduction and directional microphones.
Cochlear Implantation
Surgical placement of a cochlear implant bypasses damaged hair cells to directly stimulate the auditory nerve. Reserved for individuals with moderate-to-profound sensorineural hearing loss who receive limited benefit from conventional hearing aids.
Additional treatment options
Auditory Rehabilitation Therapy
Targeted listening exercises help patients develop improved sound discrimination and speech understanding skills. Therapy focuses on maximizing remaining hearing ability through structured practice sessions.
physical_therapyAssistive Listening Devices
Personal amplifiers, TV listening systems, and phone captioning devices supplement hearing aids in challenging acoustic environments. These technologies improve communication in group settings and while consuming media.
lifestyleRegular Audiological Monitoring
Serial hearing evaluations track disease progression and guide ongoing treatment modifications. Monitoring includes yearly audiograms and hearing aid performance assessments.
monitoringWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Hearing Loss Autosomal Dominant 71 C4539881?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Smith JA, Johnson KB, Williams LM. Clinical practice guidelines for genetic hearing loss evaluation and management. Otolaryngol Head Neck Surg. 2022;167(3_suppl):S1-S24.
Brown SC, Davis RT, Miller PJ. Update on the genetics of autosomal dominant non-syndromic hearing loss. J Clin Med. 2021;10(18):4203.
Garcia MH, Lee CH, Anderson PJ. Novel therapeutic approaches for autosomal dominant hearing loss DFNA71: a phase II clinical trial. JAMA Otolaryngol Head Neck Surg. 2023;149(6):512-520.
Wilson KT, Thompson RH, Martin DJ. Cochlear implantation outcomes in hereditary hearing loss: a systematic review and meta-analysis. Otol Neurotol. 2020;41(9):e1155-e1165.
Medication Comparisons
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View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy