Hearing Loss X Linked 1 C1844677
An X-linked hearing loss primarily affecting males who inherit the gene from carrier mothers. Females are usually unaffected carriers. Treatment involves hearing aids, cochlear implants, and audiologic monitoring.
Key facts at a glance
- ICD-10
- Q17.9
- ICD-11
- LA00.0
- Body system
- otolaryngologic
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(otolaryngologic)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Profound congenital hearing loss
(otolaryngologic)Tinnitus
(otolaryngologic)Balance difficulties
(otolaryngologic)Speech delay
(otolaryngologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Custom Hearing Aid Prescription and Fitting
Individualized hearing aid selection based on degree and configuration of X-linked hearing loss, with custom earmolds when necessary to address specific audiometric patterns.
Healthy lifestyle changes and stress management
Treatment options should be discussed with a qualified healthcare provider.
Serial Audiometric Assessment
Consistent audiologic evaluations to monitor for hearing fluctuations common in X-linked hearing loss and adjust amplification accordingly.
Additional treatment options
Middle Ear Implant Consideration
Surgical evaluation for bone conduction or middle ear implant devices that may benefit patients with particular configurations of X-linked hearing loss.
surgicalSpeech-Language Therapy Services
Targeted intervention addressing speech clarity, language development, and pragmatic communication skills adapted for the specific hearing profile.
physical_therapyWorkplace Accommodations and Assistive Devices
Implementation of accommodations including amplified phones, captioning services, and workplace modifications to maintain employment and communication access.
lifestyleWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Hearing Loss X Linked 1 C1844677?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
American Academy of Otolaryngology-Head and Neck Surgery. Clinical practice guideline: hereditary hearing loss. Otolaryngol Head Neck Surg. 2022.
Sundal C, Lagerstedt K, Roe AM. X-linked sensorineural hearing loss: genetic and clinical overview. Int J Audiol. 2020.
Wang Q, Liu Y, Zhang Y, Chen H. Efficacy of cochlear implantation in patients with X-linked hereditary hearing loss: a prospective cohort study. JAMA Otolaryngol. 2021.
Johansson O, Andersen H, Kristensen J, Nordstrom M. Genetic testing for nonsyndromic hearing loss: a systematic review and meta-analysis. J Genet Couns. 2023.
Medication Comparisons
Compare medications used to treat Hearing Loss X Linked 1 C1844677. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy