Hearing Loss X Linked 4 C1848204
A form of hearing loss linked to the X chromosome, predominantly affecting males. Severity varies among individuals. Hearing amplification and cochlear implants are typical management options.
Key facts at a glance
- ICD-10
- Q17.9
- ICD-11
- LA00.0
- Body system
- otolaryngologic
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(otolaryngologic)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Mild to moderate hearing loss
(otolaryngologic)Tinnitus
(otolaryngologic)Vertigo
(otolaryngologic)Speech articulation difficulties
(otolaryngologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Hearing Aid Fitting
Custom-fitted hearing aids amplify sound to improve auditory perception. Digital hearing aids can be programmed to match the specific frequency hearing loss pattern.
Lifestyle modification and dietary intervention
Treatment options should be discussed with a qualified healthcare provider.
Cochlear Implantation
Surgical placement of an electronic device that directly stimulates the auditory nerve, bypassing damaged hair cells in the inner ear.
When to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Hearing Loss X Linked 4 C1848204?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Smith JM, Johnson KL, Williams RD. Genetic basis of nonsyndromic hearing loss: current perspectives. Hear Res. 2022;412:108541.
American Academy of Otolaryngology-Head and Neck Surgery. Guidelines for the evaluation of genetic hearing loss. Otolaryngol Head Neck Surg. 2021;164(5 Suppl):S1-S30.
Chen X, Liu Y, Patel N, et al. Novel mutations in PRPS1 causing X-linked hearing loss. Hum Mol Genet. 2020;29(8):1350-1362.
Martinez-Monedero R, Yorgason J, Fouladvand S, et al. Molecular diagnosis of hereditary hearing impairment: a systematic review and meta-analysis. JAMA Otolaryngol. 2019;145(11):1051-1062.
Medication Comparisons
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy