Hematuria Benign Familial 1 Cn376803
A hereditary condition causing blood in the urine without kidney damage. Often runs in families. Usually requires only routine monitoring.
Key facts at a glance
- ICD-10
- Q63.9
- ICD-11
- LA00.0
- Body system
- renal
- Severity
- mild
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Gross hematuria
Changes in urination or swelling
(renal)Mild symptoms that may not significantly impact daily life.
Frequency: Common at all stages
Microscopic hematuria
(renal)Flank pain
(renal)Fatigue
(renal)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Regular Urinalysis and Blood Pressure Monitoring
Periodic monitoring of urine samples and blood pressure to track hematuria progression and ensure no complications develop. Typically involves annual or bi-annual check-ups with primary care physician.
Renal disease management
Conservative management and lifestyle modifications may be sufficient. Monitor symptoms.
Increased Hydration
Maintaining adequate fluid intake (typically 8-10 glasses daily) to dilute urine and reduce the concentration of potential irritants in the urinary tract, which may help minimize hematuria episodes.
Additional treatment options
Reduced Sodium and Oxalate Diet
Limiting high-sodium foods and oxalate-rich items such as spinach, nuts, and chocolate to reduce urinary tract irritation and support kidney health.
dietaryAvoidance of Nephrotoxic Medications
Discontinuing or substituting medications that may cause kidney irritation, such as NSAIDs, in consultation with a healthcare provider. Consider alternative pain management approaches.
medicationKidney Support Herbal Supplements
Use of traditional herbs known for urinary tract support, such as cranberry extract or stinging nettle root, though evidence is limited. Always discuss with physician before starting supplements.
complementaryWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Hematuria Benign Familial 1 Cn376803?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Kidney Disease: Improving Global Outcomes (KDIGO) Glomerular Diseases Work Group. KDIGO 2021 Clinical Practice Guideline for the Management of Glomerular Diseases. Kidney Int. 2021;100(4S):S1-S276.
Savige J, Wang Y, Arsie F, Ding J, Zhou A, Hauser M. Thin Basement Membrane Nephropathy and Benign Familial Hematuria. Kidney Int Rep. 2023;8(3):461-470.
Chen X, Anderson J, Martinez-Rivera ME, Lee K. Genetic Testing for Familial Hematuria Using Next-Generation Sequencing: A Prospective Cohort Study. Clin J Am Soc Nephrol. 2020;15(7):975-984.
Noe K, Patel D, Gonzalez-Sanchez L. Long-term Outcomes of Thin Basement Membrane Disease: A 15-Year Follow-up Study. Nephrol Dial Transplant. 2019;34(11):1867-1875.
Medication Comparisons
Compare medications used to treat Hematuria Benign Familial 1 Cn376803. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy