Hereditary C1 Esterase Inhibitor Deficiency Dysfunctional Factor C0398776
Hereditary angioedema caused by a C1 inhibitor protein that is present but does not work properly. Leads to recurrent episodes of swelling in various body parts. Managed with specific therapies and preventive measures.
Key facts at a glance
- ICD-10
- R69
- ICD-11
- MA00.0
- Body system
- immunologic
- Severity
- moderate
- Chronic
- true
Medication Comparisons
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy